( Edit )Catatan Kuliah Penyakit Jantung BawaanIngris
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Transcript of ( Edit )Catatan Kuliah Penyakit Jantung BawaanIngris
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Structures of the heart
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Normal Heart
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Atrial Septal defect( ASD )Insidence : + 10 % : ratio = 1,5 to 2 : 1Anatomy : Defect on foramen ovale : Secundum ASD Defect at SVC and RA junction: sinus venosus ASD Defect at ostium primum : primum ASD
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ASD
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Atrial Septal Defect
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Atrial Septal DefectDiagram of ASD
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LALVRVRAPAAOSystemicLungsQp > QsAtrial septal defect
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RARVLALVRARVLALVAtrial septal Defect
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Atrial septal DefectClinical findingsAsymptomaticAuscultation : Normal 1st HS or loudWidely split and fixed 2nd HSEjection systolic murmur
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Atrial Septal DefectAuscultation :1st HS N or loudwidely split and fixed 2nd HS Ejection Sistolic Murmur
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ECG : IRBB , right ventricular hypertrophyAtrial Septal Defect
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Right atrial enlargementProminence the MPA segmentIncreased pulmonary vascular marking Atrial Septal DefectChest X-Ray
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Atrial Septal DefectDiagnosis Differential
Primary Atrial Septal DefectECG : LADPartial Anomalous Pulmonary Vein DrainagePulmonary StenosisInnocent Murmur
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Atrial Septal defect
ManagementSurgery : Preschool ageRecent treatment: transcatheter closure using ASO (Amplatzer septal occluder)
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ASDSmall ShuntLarge ShuntObservationEvaluationAt age 5-8 yrsCathFR1.5ConservativeInfantsChildren/AdultsHeart Failure (-)Heart Failure (+)Age >1yrsW >10kgTranscatheter closure (Secundum ASD) /Surgical Closure(others)ConservativeAnti failureFailSuccessPH (-)PH (+)PVD (-)PVD (+)HyperoxiaReac-tiveNonreactiveSurgicalClosure
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Atrial septal defect
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Ventricular septal defectInsidence 20 % of all CHD No sex influencedAnatomy Subarterial defect : below pulmonary andaortic valve Perimembranous defect: below aortic valve at pars membranous septum Muscular defect
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VSD
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Ventricular Septal Defect
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SystemicLungsQp > QsVentricular Septal defect
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LA
LV
RV
RA
PA
AO
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RARVRALALARVLVLVVentricular septal defect
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Ventricular Septal Defect
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Ventricular Septal DefectClinical findingsDay 1st after birth: murmur (-)After 2-6 weeks : murmur (+)Murmur : pansystolic grade 3/6 or higher at LSB 3 Small muscular defect: early systolic murmurSignificant defect: Mid diastolic murmur at apex
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Small VSD Large VSD Ventricular Septal DefectMurmur: pansystolic grade 3/6 or higher at LSB 3
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Ventricular septal DefectDiagnosis Differential
PDA with PHTetralogy Fallot non cyanoticInoscent murmur
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Ventricular septal defectManagement:
Definitive : VSD closure Surgery Transcatheter closure
- DSVHeart failure (+)Heart failure (-)Anti failureFailSuccessPABEvaluate in 6 mthsSurgical closure/Transcatheter closureAortic valve prolapsInfundibular stenosisPHSmallerSpontaneousclosureCathPVD(-)PVD(+)CathCathReactiveNon-reactiveConservativeFR>1.5FR
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Patent Ductus Arteriosus Insidence+ 10%Female : Male = 1.2 to 1.5 : 1Premature and LBW higherAnatomyFetus: ductus arteriosus connects PA and aorta. If ductus does not closs Patent Ductus arteriosus
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PDA
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LALVRVRAPAAOSystemicLungsQp > QsPatent Ductus Arteriosus
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RARVLALVRALARVLVPatent Ductus Arteriosus
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Patent Ductus ArteriosusClinical findings
Small defect: Symptom (-) Growth and development normalSignificant defect:Decreased exercise tolerantWeigh gained not goodFrequent URTISpecific case: pulsus seler at 4th extremities
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Patent Ductus Arteriosus DiagnosisPulsus seler and continuous murmur heard
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Patent Ductus ArteriosusChest X- RaySimilar to VSD
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Patent Ductus ArteriosusAuscultation : continuosus murmur at upper LSB 2
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Patent Ductus ArteriosusDiagnosis DifferentialAP-windowArterio-venous fistulae
Management premature: indometasinPDA closure : surgery transcatheter closure
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PDANeonates/InfantsChildren/AdultsHeart failure (+)Heart failure (-)PrematureFull termAnti failureIndometacinSuccessFailSpontaneous closureAnti failureSuccessFailSurgical ligationTranscatheter closurePH (-)PH (+)LRRLHyperoxiaReactiveNonreactiveConservativeAge >12wksW >4kg
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Patent Ductus Arteriosus
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Patent Ductus Arteriosus
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Pulmonary Stenosis Incidence : 8-10%
Anatomy:Pulmonary stenosis valvular : Bicuspid pulmonary valve Valve leaflet thickening and adhession Pulmonary stenosis infundibular : Hyperthropy infundibulum
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Pulmonary Stenosis Clinical findingsValvular stenosis Mild : Ejection systolic Wide 2nd HS ejectiin clickModerate: ejection systolic, early systolic clickSevere : ejecstion systolic, ejection click (-) Stenosis infundibular Ejection click ( - )1st HS normal, 2nd HS weak, ejection systolic Pulmonary stenosis periphery1st & 2nd HS normal, ejection systolic
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Pulmonary StenosisMild : ejection systolic 2nd HS wide split ejection clickModerate: ejecsi systolic , early ejection click Severe : ejection systolic, click ejection (-)
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Poulmonary StenosisDiagnosisAsymptomatic patient:click systolic (stenosis valvular)systolic murmurwide split 2nd HS vary with respiration
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Pulmonary Stenosis ECG : RADEchocardiograhhy : confirmation diagnosisCatheterization: increased RV pressure without increased oxygen saturation
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Pulmonary StenosisManagement
Medicamentosa : uselessMild stenosis: intervention (-)Moderate stenosis: observationSevere stenosis: balloon valvuloplasty
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Pulmonary Stenosis
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Tetralogy FallotInsidence5-8% from all CHD
AnatomyCause: Left-anterior deviation of infundibular septum
Sindroma consist of 4 items: VSD pulmonary stenosis aortic over-riding RVH
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Tetralogy Fallot
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Tetralogy FallotHemodynamic acyanoticHemodynamic cyanotic
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Tetralogy FallotDiagnosis
Clinically : cyanosis Single 2nd HS, ejection systolic murmur
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Tetralogy FallotSingle 2nd HS, ejection systolic murmur
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Tetralogi Fallot
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Tetralogy FallotCXR : Boot-shapedConcave pulmonary segmentApex upturnedDecreased pulmonary blood flow
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Tetralogy FallotECG : RADEchocardiography : to confirm diagnosis
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Tetralogy FallotDiagnosis Differential Pulmonary Atresia Double outlet right ventricle and pulmonary stenosis Transposisi of great arteri and pulmonary stenosis
Management Paliative treatment: Blalock-Taussig shunt Definitive: total correction
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Tetralogy of Fallot< 1 yr> 1 yrspell (+)spell (-)propranololfailedsucceedBTStotal correction cathsmall PAgood sized PA clinically ECG CXR echoage 1 yrcathBTS/PDA Stentevaluation
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Tetralogy Fallot
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Tetralogy Fallot