Scleromalasi (perforans) ved RA. Sclerodaktyli CREST : calcinosis, Raynaud's phenomenon,...

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Scleromalasi (perforans) ved RA

Transcript of Scleromalasi (perforans) ved RA. Sclerodaktyli CREST : calcinosis, Raynaud's phenomenon,...

Page 1: Scleromalasi (perforans) ved RA. Sclerodaktyli CREST : calcinosis, Raynaud's phenomenon, "eosophageal" dysmotility, sclerodactyly, and telangectasia.

Scleromalasi (perforans) ved RA

Page 2: Scleromalasi (perforans) ved RA. Sclerodaktyli CREST : calcinosis, Raynaud's phenomenon, "eosophageal" dysmotility, sclerodactyly, and telangectasia.

Sclerodaktyli

Page 3: Scleromalasi (perforans) ved RA. Sclerodaktyli CREST : calcinosis, Raynaud's phenomenon, "eosophageal" dysmotility, sclerodactyly, and telangectasia.

CREST : calcinosis, Raynaud's phenomenon, "eosophageal" dysmotility , sclerodactyly, and telangectasia

Page 4: Scleromalasi (perforans) ved RA. Sclerodaktyli CREST : calcinosis, Raynaud's phenomenon, "eosophageal" dysmotility, sclerodactyly, and telangectasia.

Scleroderma species - potetrøyksopp

                                                          

Page 5: Scleromalasi (perforans) ved RA. Sclerodaktyli CREST : calcinosis, Raynaud's phenomenon, "eosophageal" dysmotility, sclerodactyly, and telangectasia.

”Slapped cheek" disease, a.k.a. fifth disease due to B19 parvovirus Other clinical syndromes include arthritis (especially in young women) and aplastic crisis in chronic hemolytic anemia

Page 6: Scleromalasi (perforans) ved RA. Sclerodaktyli CREST : calcinosis, Raynaud's phenomenon, "eosophageal" dysmotility, sclerodactyly, and telangectasia.

Rheumatoide noduli (knuter)

Page 7: Scleromalasi (perforans) ved RA. Sclerodaktyli CREST : calcinosis, Raynaud's phenomenon, "eosophageal" dysmotility, sclerodactyly, and telangectasia.

CCLE: kronisk kutan LE (=DLE) - etterlater arr !

Page 8: Scleromalasi (perforans) ved RA. Sclerodaktyli CREST : calcinosis, Raynaud's phenomenon, "eosophageal" dysmotility, sclerodactyly, and telangectasia.

Hypergammaglobulimeniske purpura ved prim Sjøgren (cf Waldenstrøm)

Page 9: Scleromalasi (perforans) ved RA. Sclerodaktyli CREST : calcinosis, Raynaud's phenomenon, "eosophageal" dysmotility, sclerodactyly, and telangectasia.

Enthesis

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Sacroileitis

Ankylosis

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Septisk artritt

Page 13: Scleromalasi (perforans) ved RA. Sclerodaktyli CREST : calcinosis, Raynaud's phenomenon, "eosophageal" dysmotility, sclerodactyly, and telangectasia.

Staphylococcus aureus septic arthritis of the left hip. The patient presented with left hip pain and fever.

(a) The initial film was normal

(b) 6 weeks later there is periarticular osteoporosis and cortical destruction of the femoral head.

Page 14: Scleromalasi (perforans) ved RA. Sclerodaktyli CREST : calcinosis, Raynaud's phenomenon, "eosophageal" dysmotility, sclerodactyly, and telangectasia.

Wegener’s granulomatosis

Page 15: Scleromalasi (perforans) ved RA. Sclerodaktyli CREST : calcinosis, Raynaud's phenomenon, "eosophageal" dysmotility, sclerodactyly, and telangectasia.

Saddle nose : trauma / polykondritt / Wegener’s granuolomatosis/ syfilis/ kokaine misbruk

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Hand artrosisheberdense – bouchardse knuter

Page 17: Scleromalasi (perforans) ved RA. Sclerodaktyli CREST : calcinosis, Raynaud's phenomenon, "eosophageal" dysmotility, sclerodactyly, and telangectasia.

Hand chondrocalcinosis

Page 18: Scleromalasi (perforans) ved RA. Sclerodaktyli CREST : calcinosis, Raynaud's phenomenon, "eosophageal" dysmotility, sclerodactyly, and telangectasia.

Livedo reticularis

Page 19: Scleromalasi (perforans) ved RA. Sclerodaktyli CREST : calcinosis, Raynaud's phenomenon, "eosophageal" dysmotility, sclerodactyly, and telangectasia.

Primaer Raynaud prevalens 5-10% , ANA neg, Norm kapillaroskopi

Page 20: Scleromalasi (perforans) ved RA. Sclerodaktyli CREST : calcinosis, Raynaud's phenomenon, "eosophageal" dysmotility, sclerodactyly, and telangectasia.

DIP ledds artritt ved psoriasis (25% of cases)

Page 21: Scleromalasi (perforans) ved RA. Sclerodaktyli CREST : calcinosis, Raynaud's phenomenon, "eosophageal" dysmotility, sclerodactyly, and telangectasia.

Positiv ANA immunofluoresence technique

Page 22: Scleromalasi (perforans) ved RA. Sclerodaktyli CREST : calcinosis, Raynaud's phenomenon, "eosophageal" dysmotility, sclerodactyly, and telangectasia.
Page 23: Scleromalasi (perforans) ved RA. Sclerodaktyli CREST : calcinosis, Raynaud's phenomenon, "eosophageal" dysmotility, sclerodactyly, and telangectasia.

ANA ELISA assay

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Erythema nodosum

Page 25: Scleromalasi (perforans) ved RA. Sclerodaktyli CREST : calcinosis, Raynaud's phenomenon, "eosophageal" dysmotility, sclerodactyly, and telangectasia.

Stage 3 sarcoidosis

Page 26: Scleromalasi (perforans) ved RA. Sclerodaktyli CREST : calcinosis, Raynaud's phenomenon, "eosophageal" dysmotility, sclerodactyly, and telangectasia.

Erytema migrans

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Cutan urinesyre ansamling = Tophi

Page 28: Scleromalasi (perforans) ved RA. Sclerodaktyli CREST : calcinosis, Raynaud's phenomenon, "eosophageal" dysmotility, sclerodactyly, and telangectasia.
Page 29: Scleromalasi (perforans) ved RA. Sclerodaktyli CREST : calcinosis, Raynaud's phenomenon, "eosophageal" dysmotility, sclerodactyly, and telangectasia.

Subakutt kutan lupus

Page 30: Scleromalasi (perforans) ved RA. Sclerodaktyli CREST : calcinosis, Raynaud's phenomenon, "eosophageal" dysmotility, sclerodactyly, and telangectasia.

Hydrops/synovia-hyperplasi i kneledd (UL)

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Rheumatoid arthritis with hyperplastic synovial villi eroding and replacing cartilage at the joint margin

Page 32: Scleromalasi (perforans) ved RA. Sclerodaktyli CREST : calcinosis, Raynaud's phenomenon, "eosophageal" dysmotility, sclerodactyly, and telangectasia.

classic "bamboo" spine

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Pølsefingre-tåer (dactylitt) ved PsA

Page 34: Scleromalasi (perforans) ved RA. Sclerodaktyli CREST : calcinosis, Raynaud's phenomenon, "eosophageal" dysmotility, sclerodactyly, and telangectasia.

Dermatomyositt

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Lupus Erythematosus - Malar eminences and nose - Malar erythema and atrophy.

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Kapillæroskopi - scleroderma

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Nailfold capillaroscopy in patients with systemic sclerosis showing changes from

normal (top left): irregular vessels, loss of some, dilation of others

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Positive C-ANCA

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TA skalp nekrosis

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Keratoderma blenorrhagicum (reaktiv artritt)

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Purpura (vaskulitt/ITP/fulminans)

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RA vaskulitt

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AMYLOIDOSISMacroglossi kutane nedslag

Page 45: Scleromalasi (perforans) ved RA. Sclerodaktyli CREST : calcinosis, Raynaud's phenomenon, "eosophageal" dysmotility, sclerodactyly, and telangectasia.

Diffuse Idiopathic Skeletal Hyperostosis, ( DISH /Forestier disease)

Page 46: Scleromalasi (perforans) ved RA. Sclerodaktyli CREST : calcinosis, Raynaud's phenomenon, "eosophageal" dysmotility, sclerodactyly, and telangectasia.

Uveitt (JRA/SpA)

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Retina vaskulitt

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Neuropathic (Charcot) arthropathy

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Libman Sacks endokarditt (SLE)

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