Incontinentia pigmenti severe X-linked genodermatosis, associated with mutations in the NEMO gene (NFkB essential modulator), affects almost exclusively.
Incontinentia pigmenti
Chapter 5 Organization and Expression of Ig Genes chain chain (n= ~85) H chain (n= ~134)
Eczema (ekzein=to boil forth ) *543 AD Inflammatory skin reaction characterized - Histologically by spongiosis Varying degrees of acanthosis,
