PJB, PNEUMONIA INA 25desember15.ppt

download PJB, PNEUMONIA INA 25desember15.ppt

of 45

Transcript of PJB, PNEUMONIA INA 25desember15.ppt

  • 8/18/2019 PJB, PNEUMONIA INA 25desember15.ppt

    1/45

    Laporan Jaga

    Jumat Pagi, 25 Desember 2015

    dr Ony /dr. Argadr. Anggra /dr. Cempaka/dr. Prabu/ dr

    Iqbal

    dr. Febry/dr. David

    dr. Indra

  • 8/18/2019 PJB, PNEUMONIA INA 25desember15.ppt

    2/45

    Bangsal1. An. J, lelaki, 5 bulan/5 kg dengan

    pneumonia dd bronkhiolitis, DE: PJBasianotik; DA: AD !!, "# moderate; D$:%&'A !!; do(n s)ndrome ; undensensus

    testi*ulorum unilateral; gi+i baikunder(eight normoheight2. An D, perempuan, 15 taun/ 5! kg dengananemia apla"tika# gi$i baik normoweight

    normoheight 

    '- pediatri 0

    %!- 0

  • 8/18/2019 PJB, PNEUMONIA INA 25desember15.ppt

    3/45

    Identitas

    %ama & An. '

     'eni" (elamin & )elaki

    *mur & 5 bulan

    Alamat & +anak 1 -/- !2/!2 0ebyk,(aranganyar

    % - & !1312143

    ++/+ & 5kg / ! m

  • 8/18/2019 PJB, PNEUMONIA INA 25desember15.ppt

    4/45

    Keluhan Utama

    6e"ak %a7a"

  • 8/18/2019 PJB, PNEUMONIA INA 25desember15.ppt

    5/45

  • 8/18/2019 PJB, PNEUMONIA INA 25desember15.ppt

    6/45

    • ± % hari SMRS, pasien mengeluh sesak dan batuk semakinsering. !asien masih demam, turun bila diberikan obat

     penurun panas,tetapi kembali demam setelah beberapa $amkemudian, pasien tidak ada keluhan pilek, muntah ataupun

    diare. BAK dan BAB tidak ada keluhan. BAK #&'(hari

    warna kuning $ernih. BAB )#%'(hari dengan ampas

    ke*okelatan.• ) hari SMRS, pasien terlihat semakin sering batuk dan sesak .!asien pun masih mengeluh demam naik turun. !asien tidak

    ada keluhan pilek, muntah dan diare. BAK dan BAB tidak ada

    keluhan. +ikarenakan pasien semakin sesak, pasien berobat ke

    RS+M.

    • Saat di -+, pasien tampak gelisah, sesak, batuk, tidakdemam. BAK tidak ada keluhan. BAB terakhir )' MRS

    dengan ampas kuning ke*okelatan.

  • 8/18/2019 PJB, PNEUMONIA INA 25desember15.ppt

    7/45

    Riwaat Pena!it Dahulu

    • -i8ayat "erupa & 9:;

    • -i8ayat mndk & 9:; dengan

    diagn"a P'+ a"iantik, A6D II -mderate, D8n "indrm klini"

  • 8/18/2019 PJB, PNEUMONIA INA 25desember15.ppt

    8/45

    Riwaat Pena!it Keluarga

    •-i8ayat keluarga dengankeluan "erupa9

  • 8/18/2019 PJB, PNEUMONIA INA 25desember15.ppt

    9/45

    Riwaat Kehamilan dan Persalinan

    • 6elama amil ibu pa"ien rutin kntrl kepu"ke"ma" dan rutin meminum vitamin yangdiberikan

    • -i8ayat "akit "elama amil di"angkal

    • Pa"ien lair "eara "pntan ditlng bidan padaumur keamilan > bulan dengan ++) 24!! gram P+? m

    • 6aat lair pa"ien lang"ung menangi", tidak birudengan ketuban =erni

    (e"an& ri8ayat keamilan dan kelairan dalam bata"nrmal

  • 8/18/2019 PJB, PNEUMONIA INA 25desember15.ppt

    10/45

    Riwaat Imunisasi

    • @ep + & ! bulan

    • +C0 & 1 bulan

    • DP/@i+ & 2, 3, ? bulan

    • Pli & 1, 2, 3, ? bulan

    (e"an & imuni"a"i "e"uai =ad8al Depke"

  • 8/18/2019 PJB, PNEUMONIA INA 25desember15.ppt

    11/45

    Riwaat #utrisi

    6aat ini pa"ien minum "u"u 7rmula"e=ak lair dengan

    7rekuen"i 4 kali "ebanyak 2!

  • 8/18/2019 PJB, PNEUMONIA INA 25desember15.ppt

    12/45

    Pohon Keluarga

    I

    II

    III

    Tn O, 45 thn

     An. J 5 bulan, 5kg

    Ny Y, 43 thn

  • 8/18/2019 PJB, PNEUMONIA INA 25desember15.ppt

    13/45

    Pemeri!saan $isis(eadaan umum & tampak "akit "edang, "e"ak, mp" menti", gi$i baik

    ital "ign &la=u nadi& 12! B/menit 6atura"i& > >19i"i dan tekanan ukup; >1 >2

     la=u napa"& 54 B/menit

    9reguler dan kedalaman ukup;

     "uu& 3,? C perak"ilar

    (epala & nrme7al, )( 3 m 9

  • 8/18/2019 PJB, PNEUMONIA INA 25desember15.ppt

    14/45

    r & I & Iktu" krdi" tidak tampak

    P & IC teraba di 6IC I )C6, tidak kuat angkat

    P & bata" =antung "ulit dievalua"i  A & +' I

  • 8/18/2019 PJB, PNEUMONIA INA 25desember15.ppt

    15/45

    Btremita" & Akral Dingin &

  • 8/18/2019 PJB, PNEUMONIA INA 25desember15.ppt

    16/45

    "tatus %i&i

    • ++/* & 5/.3B 1!! G > 9P5E++/*EP25;under8eigt

    •  +/* & !/3 B 1!! G >5 9+/*G P25;

    nrmeigt• ++/+ & 5/5.> B 1!! G 4? 9++/+G P25; gi$i

    baik

    • (e"impulan & gi$i baik, underweight, normoheight 

  • 8/18/2019 PJB, PNEUMONIA INA 25desember15.ppt

    17/45

    Da'tar (asalahSeorang anak lelaki (/ bulan (/ kg0

    ).  Sesak hari%.  batuk 7 hari

    . +emam hari

    &. low nasal bridge

    /. 1a2as *uping hidung "

    3. low set ears

    7. retraksi 4"5 sub*ostal

    6. Suara na2s tambahan 0 RBK 4"("5, wheeing 4"("5, RB sulit die8aluasi

    9. bising 4"5 sistolik grade %(3 !M di S: ;!SS

    )

  • 8/18/2019 PJB, PNEUMONIA INA 25desember15.ppt

    18/45

    DI)%#*"I" +)#DI#%

    ). !neumonia dd bronkhiolitis

    %. Sindrom down 4klinis5

    . ?sk SK 

    &. =ndesensus testis unilateral

  • 8/18/2019 PJB, PNEUMONIA INA 25desember15.ppt

    19/45

    Laboratorium• @b & 11.2 g/dl

    •@C & 32 • A) & .4 ribu/ul

    • A & 2? ribu/ ul

    • A & 3.>  'uta/ul

    • C & 41.? /um

    • C@ & 24.3 pg

    • C@C & 3?.4 g/dl• -D &12.>

    • P & .5 K

    • PD & 1 

    • "/ +a"/ %et/ )im7 / n & !.?/ !.3/ 51.?/?3./?.2! 9;

    • 0D6 & 1!4 mg/dl

    (e"an & dalam bata" nrmal

  • 8/18/2019 PJB, PNEUMONIA INA 25desember15.ppt

    20/45

    R* hora-

    Kesan: menyokong pneumonia

    Cor tak tampak membesar 

  • 8/18/2019 PJB, PNEUMONIA INA 25desember15.ppt

    21/45

    Diagnosis !er.a).!neumonia

    %.+>0 !@B asianotik 

    +A0 AS+ , ?R moderate+0 ROSS

    .?sk SK 

    &.Sindrom down 4klinis5

    /.=ndesensus testis unilateral

    3.-ii baik, underweight, normoheight

  • 8/18/2019 PJB, PNEUMONIA INA 25desember15.ppt

    22/45

    erapi

    • -a8at bang"al kardilgi• O2 na"al 2 lpm

    • A6I/A6+ 4B 3! via %0

    • In7 D1/? %6 12 /=am

    • In=ek"i ampiillin 925 mg/kg/ =am;G 125 mg/ =am• In=ek"i gentamiin lading d"e 94mg/kg;G ?! mg,"elan=utnya 95mg/kg/2? =am;G 25 mg/2? =am

    • Paraetaml 91!mg/kg/kali;G 5! mg via %0

    • Drner 2B 1/1! tab per ral

    • Fur"emide 2B 2 mg tab per ral

    • 6pirnlatn 2B 3,125 mg tab per ral

    • %ebuli$er %aCl !,> 5 /4 =am

  • 8/18/2019 PJB, PNEUMONIA INA 25desember15.ppt

    23/45

    Plan*rinali"a / 7e"e" rutin

    nitring• (*/6/"i2/?=am• +CD/4=am

  • 8/18/2019 PJB, PNEUMONIA INA 25desember15.ppt

    24/45

    $ollow Up, "abtu 2/ Desember 2015(eadaan umum & tampak "akit "edang, "e"ak, mp" menti", gi$i baik

    ital "ign &la=u nadi& 12! B/menit 6atura"i& > >19i"i dan tekanan ukup; >1 >2

     la=u napa"& 54 B/menit

    9reguler dan kedalaman ukup;

     "uu& 3,? C perak"ilar

    (epala & nrme7al,)( 3 m 9

  • 8/18/2019 PJB, PNEUMONIA INA 25desember15.ppt

    25/45

    r & I & Iktu" krdi" tidak tampak

    P & IC teraba di 6IC I )C6, tidak kuat angkat

    P & bata" =antung "ulit dievalua"i  A & +' I

  • 8/18/2019 PJB, PNEUMONIA INA 25desember15.ppt

    26/45

    Btremita" & Akral Dingin &

  • 8/18/2019 PJB, PNEUMONIA INA 25desember15.ppt

    27/45

    Diagnosis !er.a).!neumonia

    %.+>0 !@B asianotik 

    +A0 AS+ , ?R moderate+0 Ross

    .?sk SK 

    &.Sindrom down 4klinis5

    /.=ndesensus testis unilateral

    3.-ii baik, underweight, normoheight

  • 8/18/2019 PJB, PNEUMONIA INA 25desember15.ppt

    28/45

    erapi

    • O2 na"al 2 lpm 9k/p;• A6I/A6+ 4 B 3! via %0

    • In7 D1/? %6 12 /=am

    • In=ek"i ampiillin 925 mg/kg/ =am;G 125 mg/ =am 9II;

    • In=ek"i gentamiin 95mg/kg/2? =am;G 25 mg/2? =am 9II;

    • Paraetaml 91!mg/kg/kali;G 5! mgG 3 t L tk.p via %0

    • Drner 2B 1/1! tab per ral

    • Fur"emid 2B 2 mg tab per ral

    • 6pirnlatn 2B 3,125 mg tab per ral

    • %ebuli$er %aCl !,> 5 /4 =am

  • 8/18/2019 PJB, PNEUMONIA INA 25desember15.ppt

    29/45

  • 8/18/2019 PJB, PNEUMONIA INA 25desember15.ppt

    30/45

    +agaimana!ah prognosa pasien downsndrom dengan PJ+ P : anak dengan down syndo!

    I : "

    # : "

    O : 5 yeas su$%$al ate anak down syndo!dengan PJ&

  • 8/18/2019 PJB, PNEUMONIA INA 25desember15.ppt

    31/45

    Survival analysis of Down syndrome with

    congenital heart disease: a 5-years registry atQSNICH.Layangool T, Sangtawesin C, Kirawittaya T, Prompan W, Prachasilchai P,

    Pechdamrongsakul A!C"#$%&ND: !own syndrome "!S# is the most common chromosomal abnormality

    in children Atrio$%entricular septal de&ect "A'S!# is the most common congenital heart

    disease "C(!# reported in !S The mortality rate o& !S with congenital heart disease"C(!# is )$* times higher than normal population The sur%i%al rate in !S has impro%ed

    with time and has reported up to +- and .)- at one and ten years o& age,

    respecti%ely

    %'(C)I*(: To study the pre%alence o& C(!, clinical course, treatment, the o%erall

    sur%i%al in patients with !S compare with those who are associated with C(!

    +!)($I!, !ND +()H%D: All !S patients at /S01C( with parental signed consent

    were enrolled in the registry The study was conducted &or ) years starting &rom 2ay

    344* to April 343 All patients were &ollowed$up according to schedule modi&ied &rom

     American Academic o& Pediatrics "AAP# health super%ision guideline Standard

    treatment was gi%en to all those children with diagnosis o& C(! and5or other associated

    diseases

  • 8/18/2019 PJB, PNEUMONIA INA 25desember15.ppt

    32/45

    $(S&,)S: 6our hundred and two cases o& !S were enrolled Two cases were e7cluded due

    to the parental incon%enience The mode and mean age o& the patients at registration were

    and * months "$83# Two hundred and se%enty$one cases had an initial

    echocardiographic diagnosis o& C(!, which included + o& Patent ductus arteriosus "P!A#,9+ o& 'entricular septal de&ect "'S!#, 9 o& A'S!, 9 o& secondum Atrial septal de&ect

    "AS!#, 8 o& Tetralogy o& 6allot "T;6#, 3 o& Coractation o& Aorta "CoA#, o& other C(! and

    99 o& combined lesions !uring the &ollow$up period, spontaneous closure o& P!A, 'S! and

     AS! occurred in 98, 3 and ) cases, respecti%ely A&ter the e7clusion o& those who had

    spontaneous closure, the pre%alence rate o& C(! in !S was 9+.- 'S! was the most

    common lesion, slightly more than P!A 0inety$eight cases underwent cardiac surgery<

    including + o& associated 'S!, 39 o& A'S!, 38 o& P!A, o& T;6, 9 o& CoA5AA repaired,one each o& Cor triatriatum and primum AS! Twel%e cases had catheter inter%entions,

    including P!A occlusion "4 cases#, and case o& balloon dilatation o& re$CoA and coils

    emboli=ation o& isolated ma>or aorto$pulmonary collateral artery Se%en cases were lost at

    &ollow$up ?y using the hospital in&ormation and 0ational (ealth Security ;&&ice "0(S;#

    database, 9* in&ants died during the &ollow$up period The causes o& death were immediate

    post cardiac surgery in 4 cases "A'S! in +, 'S! in # and not associated with surgery in

    * cases including C(6 in ., pneumonia in *, leukemia in 9, airway disease in , others *and unknown . cases The o%erall sur%i%al at and ) years o& age were +8- and .8-,

    respecti%ely !S with C(! had a signi&icantly lower sur%i%al rate than those without C(! "p

    @ 444#

    C%NC,&SI%N: According to this study, the revalence rate of CHD in DS was high. *SD

    was the most common lesion and has better prognosis than A'S! )he main cause of

    death was a cardiac rolem. 6ollow$up patients by using modi&ied AAP guideline and

    standard treatment can impro%e their o%erall sur%i%al

  • 8/18/2019 PJB, PNEUMONIA INA 25desember15.ppt

    33/45

  • 8/18/2019 PJB, PNEUMONIA INA 25desember15.ppt

    34/45

  • 8/18/2019 PJB, PNEUMONIA INA 25desember15.ppt

    35/45

  • 8/18/2019 PJB, PNEUMONIA INA 25desember15.ppt

    36/45

  • 8/18/2019 PJB, PNEUMONIA INA 25desember15.ppt

    37/45

  • 8/18/2019 PJB, PNEUMONIA INA 25desember15.ppt

    38/45

  • 8/18/2019 PJB, PNEUMONIA INA 25desember15.ppt

    39/45

  • 8/18/2019 PJB, PNEUMONIA INA 25desember15.ppt

    40/45

  • 8/18/2019 PJB, PNEUMONIA INA 25desember15.ppt

    41/45

  • 8/18/2019 PJB, PNEUMONIA INA 25desember15.ppt

    42/45

  • 8/18/2019 PJB, PNEUMONIA INA 25desember15.ppt

    43/45

    • '%ld to !odeately edu(ed T (ell (ounts

    • '%ld to !odeately edu(ed & (ell (ounts

    • Absen(e o) no!al ly!*ho(yte e+*ans%on %n %n)an(y 

    • Thy!us s%e %s s!alle than age"!at(hed (ontols

    • '%ld to !odeately edu(ed na%$e T (ell *e(entages, w%th (oes*ond%ng edu(t%on o) T (ell e+(%s%on (%(les-Te(s

    • /ubo*t%!al ant%body es*onses to %!!un%at%ons

    • 0e(eased total and s*e(%)%( %!!unoglobul%n A %n sal%$a• 0e(eased neuto*h%l (he!ota+%s

    1mmune de&ects in !own syndrome

  • 8/18/2019 PJB, PNEUMONIA INA 25desember15.ppt

    44/45

  • 8/18/2019 PJB, PNEUMONIA INA 25desember15.ppt

    45/45

    erima Kasih