Malrotation - SUNY Downstate Medical Centerdownstatesurgery.org/files/cases/malrotation_kate.pdf ·...
Transcript of Malrotation - SUNY Downstate Medical Centerdownstatesurgery.org/files/cases/malrotation_kate.pdf ·...
MalrotationMalrotation
Kate Sinnott, MDDepartment of Surgery
Downstate Medical CenterDownstate Medical Center8/20/2009
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GI Causes of Vomiting in gInfant/Child
Bilious Nonbilious
Intussusception GastroenteritisIntussusception GastroenteritisMalrotation w/ volvulus GERDIncarcerated Hernia Hepatobiliary N t P titiNeonate PancreatitisHirschsprung’s GastroparesisNEC PUDCongenital Atresia AppendicitisMeconium Ileus Neonate
Pyloric StenosisPyloric Stenosis
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Normal Gut Rotationwww.downstatesurgery.org
Normal Gut Roationwww.downstatesurgery.org
Normal Gut Rotationwww.downstatesurgery.org
Abnormal Gut RotationAbnormal Gut Rotation
• NonrotationNonrotation • When both limbs return to abdomen without furrther rotation• Small bowel on right and colon on left
Wid t l i k f l l• Wide mesentery – less risk of volvulus• Gastroschisis; Omphalocele; Diaphragmatic Hernia
• MalrotationMalrotation• Duodenojejunal limb remains in nonrotation in the right
midabdomenCecocolic limb in partial rotation in the midupper abdomen• Cecocolic limb in partial rotation in the midupper abdomen fixed to abdominal wall by Ladds bands
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Abnormal Gut Rotationwww.downstatesurgery.org
Pathophysiology of MalrotationPathophysiology of Malrotation
• VolvulusVolvulus – Twisting of the small bowel about the
mesentery causing ischemiamesentery causing ischemia– Life threatening surgical emergency
• ObstructionL dd’ B d i th– Ladd’s Bands securing cecum cross the duodenum
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P t ti f M l t tiPresentation of Malrotation
• 50% cases in infants less than 1month• 50% cases in infants less than 1month present with volvulus•10-15% cases in older children present with10 15% cases in older children present with volvulus•Symptoms of Obstruction
–vomiting; abdominal pain; distention•Symptoms of Volvulus –
iti (bili bili ) t–vomiting (bilious or nonbilious) most common symptom–Sepsis caused by bowel necrosisp y
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Presentation of Malrotation in Older Children and Adults
•Variable and insidious•Intermittent abdominal pain/ vomiting•Failure to thriveFailure to thrive•Chronic diarrheaP titi•Pancreatitis
•Malabsorption
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M l t tiMalrotation
XXray
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UGIS Fi di i M l t tiUGIS Findings in Malrotation
•
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B i EBarium Enema
•
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CT S Fi di i M l t tiCT Scan Findings in Malrotation
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CT S Fi di i M l t tiCT Scan Findings in Malrotation
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S i l M t f M l t tiSurgical Management of Malrotation
L dd P dLadd Procedure–-goal is not to return bowel to normal
fi ticonfiguration–Prevent risk of volvulus
Wid h b f h–Widen the base of the mesentary–Placement of bowel in the position of
t ti ith ll b l i ht dnonrotation with small bowel on right and colon on leftAppendectomy-Appendectomy
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L i L dd P dLaparoscopic Ladd Procedure
O l f d i th b f•Only performed in the absence of volvulus or bowel ischemia
•May be associated with higher y grecurrence rate due to fewer adhesions
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Surgical Management of Incidental g gAsymptomatic Malrotation
C t i l•Controversial•Difficulty to determine width of mesentary and risk of volvulus by imaging •Most recommend laparocopic surgery for assessment of width of mesentary in yasymptomatic malrotation regardless of age or presenting symptomsg p g y p
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R fReferences
1 Sabiston’s Te tbook of S rger To nsend1. Sabiston’s Textbook of Surgery. Townsend et al. Chapter 71
2 Up To Date Intestinal Malrotation Mary L2. Up To Date. Intestinal Malrotation. Mary L. Brandt. May 2009
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