Intracranial dural av fistula with spinal perimedullary venous drainage rare case

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tion of Interventional & Neuroradiolog C & Sir JJ Hospital, Byculla, Mumbai Dr. Prashant Pote (JR2) Dr. Avinash Gutte (Asst. Pro

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Intracranial dural av fistula with spinal perimedullary venous drainage rare case

Transcript of Intracranial dural av fistula with spinal perimedullary venous drainage rare case

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Section of Interventional & NeuroradiologyGGMC & Sir JJ Hospital, Byculla, Mumbai

Dr. Prashant Pote (JR2)Dr. Avinash Gutte (Asst. Prof)

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26 yrs/M---- From Neurology C/o gradual but rapidly progressive quadreparesis since 3 weeks.C/o Decreased respiratory drive since 2 days.No past major illness.

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MRI T2 images showing cord swelling central hyperintensity taking the shape of the central grey matter

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After contrast injestion, dilated enhanced perimedullary veins were observed on the surface of the spinal cord

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MRI interpretation…DDxSPINAL DAFINTRAMEDULARY AVMINTRAMEDULLARY AVFFORAMNEG MAGNUM DAFPARA-SPINAL AVM

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ASA

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Final diagnosis Intracranial DAVF fed by

meningohypophyseal trunk and MMA with spinal perimedullary venous drainage.

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Treatment option:Occlusion of fistula with liquid embolic

agent(Onyx).

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References: Doppman J L, G Di Chiro and E H Oldfield. “Origin of spinal

arteriovenous malformation and normal cord vasculature from a common segmental artery: angiographic and therapeutic considerations..” Radiology 154, no. 3 (March 1985): 687-689

Minami S, T Sagoh, K Nishimura et al. “Spinal arteriovenous malformation: MR imaging..” Radiology 169, no. 1 (October 1988): 109-115. doi:VL - 169.

Mullan S. Reflections upon the nature and management of intracranial and intraspinal vascular malformations and fistulae. J Neurosurg. 1994;80:606–616.[PubMed]

Teng MM, Chang T, Lirng JF et-al. Spinal dural arteriovenous anomalies. J Vasc Interv Radiol. 1992;3 (2): 329-36

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Thank you!