Disorders of Skeletal System
description
Transcript of Disorders of Skeletal System
SEMINAR ON
ANOMALIES OF SKELETAL SYSTEM
TALIPES AND DEVELOPMENTAL
DYSPLASIA OF HIP
SUBMITTED TO SUBMITTED BY
Mrs.Deepa.P Ms.Sreekala.R
Asst.Professor 2nd year MSc Nursing Student
Govt.College Of Nursing Govt.College Of Nursing
Alappuha Alappuha
SUBMITTED ON
08/03/2016
1
ANOMALIES OF SKELETAL SYSTEM
TALIPES AND DEVELOPMENTAL DYSPLASIA OF HIP
INTROUCTION:
Some skeletal defects may be diagnosed at birth or within days, weeks, or months after birth. In
other cases, the deviation may be difficult to detect without careful inspection. Therefore, it is
imperative that nurses become acquainted with signs of these defects and understand the
principles of therapy in order to direct others in the care and management of these children.
DEVELOPMENTAL DYSPLASIA OF THE HIP
The broad term developmental dysplasia of the hip (DDH) describes a spectrum of disorders
related to abnormal development of the hip that may occur at any time during fetal life, infancy,
or childhood. A change in terminology from congenital hip dysplasia and congenital dislocation
of the hip to DDH more properly reflects a variety of hip abnormalities in which there is a
shallow acetabulum, subluxation, or dislocation.
EPIDEMIOLOGY
o Incidence
most common orthopaedic disorder in newborns
dysplasia is 1:100
dislocation is 1:1000
o Location
most common in left hips in females
bilateral in 20%
o Demographics
more commonly seen in Native Americans and Laplanders
rarely seen in African Americans
o Risk factors
2
first born
female (6:1 over males)
breech
family history
oligohydramnios
CLASSIFICATION
1. Acetabular dysplasia—This is the mildest form of DDH, in which there is neither
subluxation nor dislocation. There is a delay in acetabular development evidenced by
osseous hypoplasia of the acetabular roof that is oblique and shallow, although the
cartilaginous roof is comparatively intact. The femoral head remains in the acetabulum.
2. Subluxation—The largest percentage of DDH, subluxation, implies incomplete
dislocation of the hip and is sometimes regarded as an intermediate state in the
development from primary dysplasia to complete dislocation. The femoral head remains
in contact with the acetabulum, but a stretched capsule and ligamentum teres cause the
head of the femur to be partially displaced. Pressure on the cartilaginous roof inhibits
ossification and produces a flattening of the socket.
3. Dislocation—The femoral head loses contact with the acetabulum and is displaced
posteriorly and superiorly over the fibrocartilaginous rim. The ligamentum teres is
elongated and taut.
3
PATHOPHYSIOLOGY
The cause of DDH is unknown, but certain factors such as gender, birth order, family history,
intrauterine position, delivery type, joint laxity, and postnatal positioning are believed to affect
the risk of DDH.
Predisposing factors associated with DDH may be divided into three broad categories:
(1) Physiologic factors, which include maternal hormone secretion and intrauterine positioning;
(2) mechanical factors, which involve breech presentation, multiple fetus, oligohydramnios, and
large infant size (other mechanical factors may include continued maintenance of the hips in
adduction and extension that will in time cause a dislocation); and
(3) Genetic factors, which entail a higher incidence of DDH in siblings of affected infants and
an even greater incidence of recurrence if a sibling and one parent were affected.
Some experts categorize DDH into two major groups:
(1) Idiopathic, in which the infant is neurologically intact, and
(2) Teratologic, which involves a neuromuscular defect such as arthrogryposis or
myelodysplasia. The teratologic forms usually occur in utero and are much less common.
CLINICAL MANIFESTATIONS
Infants
Shortening of limb on affected side (Galeazzi sign)
Restricted abduction of hip on affected side
Unequal gluteal folds (best visualized with infant prone)
Positive Ortolani test (hip is reduced by abduction)
Positive Barlow test (hip is dislocated by adduction)
Older Infants and Children
Affected leg appears shorter than the other
Telescoping or piston mobility of joint—Head of femur felt to move up and down in
buttock when extended thigh is pushed first toward child’s head and then pulled distally
Trendelenburg sign—When child stands first on one foot and then on the other (holding
onto a chair, rail, or someone’s hands) bearing weight on affected hip, pelvis tilts
downward on normal side instead of upward, as it would with normal stability
4
Greater trochanter prominent and appearing above a line from anterosuperior iliac spine
to tuberosity of ischium
Marked lordosis and waddling gait (bilateral hip dislocation)
DIAGNOSTIC EVALUATION
Physical exam (< 3 months)
o mainstay of physical diagnosis is palpable hip subluxation/dislocation on exam
Barlow
dislocates a dislocatable hip by adduction and depression of the flexed femur
Ortolani
reduces a dislocated hip by elevation and abduction of the flexed femur.
Galeazzi (Allis)
apparent limb length discrepancy due to a unilateral dislocated hip with hip and knee
flexed at 90 degrees
femur appears shortened on dislocated side
hip clicks are nonspecific findings
Barlow and Ortolani a rarely positive after 3 months of age because of soft-tissue
contractures about the hip
Physical exam (> 3 months)
5
limitations in hip abduction
most sensitive test once contractures have began to occur
occurs as laxity resolves and stiffness begins to occur
decreased symmetrically in bilateral dislocations
leg length discrepancy predominate
Physical exam (> 1 year - walking child)
pelvic obliquity
lumbar lordosis in response to hip contractures resulting from bilateral dislocations in a
child of walking age
Trendelenburg gait results from abductor insufficiency
toe walking compensate for relative shortening of affected side
IMAGING
6
Radiograph
It becomes primary imaging modality at 4-6 month after the femoral head begins to ossify
HIP DISLOCATION
Hilgenreiner's line
It is a horizontal line through right and left triradiate cartilage ,femoral head ossification should
be inferior to this line
Perkin’s line
It is a perpendicular line to Hilgenreiner's through a point at lateral margin of acetabulum
femoral head ossification should be medial to this line
Shenton's line
It is an arc along inferior border of femoral neck and superior margin of obturator foramen ,arc
line should be continuous. delayed ossification of the femoral head is seen in cases of
dislocation
7
HIP DYSPLASIA
Acetabular index (AI)
It is an angle formed by a line drawn from point on the lateral triradiate cartilage to point on
lateral margin of acetabulum and Hilgenreiners line. It should be less than 25° in patients older
than 6 months.
Center-Edge Angle (CEA) Of Wiberg
It is an angle formed by a vertical line from the center of the femoral head and a line from the
center of the femoral head to the lateral edge of the acetabulum ,less than 20° is considered
abnormal . It is reliable only in patients over the age of 5 years.
8
•Ultrasound
It evaluates for acetabular dysplasia and/or the presence of a hip dislocation and is useful before
femoral head ossification (<4-6 mos). It may produce spurious results if performed before 4-6
weeks of age. It allows view of bony acetabular anatomy, femoral head, labrum, ligamentum
teres, hip capsule .
Alpha Angle
It is an angle created by lines along the bony acetabulum and the ilium. Norrmal is greater than
60. °
Beta Angle
It is an angle created by lines along the labrum and the ilium. Normal is less than 55°, femoral
head is normally bisected by a line drawn down from the ilium. It is used as an adjunct only in
patients at 3-4 weeks in patients who are considered high risk (family history and/or have an
equivocal physical exam). Normal ultrasound in patients with soft-tissue 'clicks' will have normal
acetabular development. It allows for monitoring of reduction during Pavlik harness treatment. It
is not cost effective for routine screening
9
Arthrogram
It is used to confirm reduction after closed reduction under anesthesia. It helps to identify
possible blocks to reduction, inverted labrum, labrum enhances the depth of the acetabulum by
20% to 50% and contributes to the growth of the acetabular rim.In the older infant with DDH the
labrum may be inverted and may mechanically block concentric reduction of the hip, inverted
limbus. It represents a pathologic response of the acetabulum to abnormal pressures caused by
superior migration of the head, consists of fibrous tissue, transverse acetabular ligament, hip
capsule is constricted by iliopsoas tendon causing hour-glass deformity of the capsule, pulvinar,
ligamentum teres.
CT
CT study of choice to evaluate reduction after closed reduction and spica casting
MRI
It does not play significant role in primary diagnosis.
TREATMENT
• Nonoperative
Abduction Splinting/Bracing (Pavlik Harness)
Indications
DDH < 6 months of age and reducible hip
Pavlik harness treatment is contraindicated in teratologic hip dislocations
It is a dynamic splint that requires normal muscle function for successful outcomes
It is contraindicated in patients with spina bifida or spasticity
outcomes
10
overall Pavlik harness has success rate of 90%
dependent upon age at initiation of treatment and time spent in the harness
abandon pavlik harness treatment if not successful after 3-4 weeks
If pavlik harness fails, convert to semi-rigid abduction brace with weekly ultrasounds for an
addition 3-4 weeks before considering further intervention.
Closed Reduction And Spica Casting
Indications
DDH in 6 - 18 months of age
failure of Pavlik treatment
OPERATIVE
open reduction and spica casting
Indications
DDH in patient >18 months of age
failure of closed reduction
open reduction and femoral osteotomy
Indications
DDH > 2 yr with residual hip dysplasia
anatomic changes on femoral side (e.g., femoral anteversion, coxa valga)
femoral head should be congruently reduced with satisfactory ROM, and reasonable
femoral sphericity
best in younger children (< 4 yr)
11
after 4 yr, pelvic osteotomies are utilized
open reduction and pelvic osteotomy
Indications
DDH > 2 yr with residual hip dysplasia
severe dysplasia accompanied by significant radiographic changes on the acetabular side
(increased acetabular index)
used more commonly in older children (> 4 yr)
decreased potential for acetabular remodeling as child ages.
Abduction splinting/bracing (Pavlik harness)
Goals
Ttreatment is based on early concentric reduction in order to prevent future degeneration of
the hip.
Risk, complexity and complications are increased with delays in diagnosis
Position in bracing
goal is 90-100° flexion (controlled by anterior straps) and abduction of 50° (controlled by
posterior straps)
discontinue if hip is not reduced by 3-4 weeks to prevent Pavlik disease- erosion of the
pelvis superior to the acetabulum and prevention of the development of the posterior wall
of the acetabulum, worn for 23 hours/day for at least 6 weeks or until hip is stable
wean out of harness over 6-8 weeks after hip has stabilized until normal anatomy
develops.
confirm position with ultrasound or xray and monitor every 4-6 week
• Closed reduction and spica casting
o performed under general anesthesia
12
o arthrogram used to confirm reduction
concentric reduction must be obtained with less than 5mm of contrast pooling medial to
femoral head and the limbus must not be interposed
the arthrogram will also help identify anatomic blocks to reduction:
spica casting
following reduction immobilize in a spica cast with hip flexion of 100 deg. and abduction
of 45 deg with neutral rotation for 3 months
'human position'
change cast at 6 weeks
adductor tenotomy performed if patient has an unstable safe zone
used if excessive abduction required to maintain the reduction
confirm reduction with CT scan in spica cast with selective cuts to minimize radiation to
the child
• Open reduction
o anterior approach (Smith-Peterson) most common to decrease risk to medial femoral
circumflex artery
capsulorrhaphy can be performed after reduction
used if patient is older than 12 months
o other possible approaches include
medial adductor approach, variation of Ludloff
13
Pros
directly addresses block to reduction
can be used in patients under 12 months of age
less blood loss
Cons
unable to perform a capsulorrhaphy
higher association of AVN
anteromedial approach
posteromedial approach
o remove possible anatomic blocks to reduction
iliopsoas contracture, capsular constriction, inverted labrum, pulvinar, hypertrophied
ligamentum teres
o adductor tenotomy performed if patient has an unstable safe zone
if excessive abduction required to maintain the reduction
o immobilize in functional position of 15° of flexion, 15° of abduction and neutral rotation
• Femoral Osteotomy
o used to correct excessive femoral anteversion and/or valgus
o femoral osteotomy and shortening may be needed to prevent AVN
decrease tension produced by reduction of a previously dislocated hip
14
• Pelvic Osteotomies
o increase anterior or anterolateral coverage
o used after reduction is confirmed on abduction-internal rotation views and satisfactory
ROM has been obtained.
15
16
Indication Technique
Salter Younger patients
typically with open
triradiate cartilage
Single cut above acetabulum through the ilium to sciatic
notch. Acetabulum hinges through the pubic symphysis.
The redirectional osteotomy can provide 20-25° lateral
and 10-15° anterior coverage (coverage limitations in
anterolateral head). May lengthen leg up to 1 cm.
Triple(Steele) Favored in older children
because their symphysis
pubis does not rotate
well. Performed when
open triradiate cartilages
are present
Salter osteotomy plus additional cuts through superior
and inferior pubic rami. Acetabular reorientation
procedure.
PAO (Ganz) Triradiate cartilage must
be closed in order to
perform
Involves multiple osteotomies in the pubis, ilium, and
ischium near the acetabulum. This allows improved three-
dimensional correction of the acetabulum configuration.
It is technically the most challenging. Posterior column
and pelvic ring remain intact and patients are allowed to
weight bear early
Pemberton For moderate to severe
DDH; most versatile;
triradiate cartilage must
be open
Osteotomy starts approximately 10 to 15 mm above the
AIIS, proceeds posteriorly, and ends at the level of the
ilioischial limb of the triradiate cartilage (halfway
between the sciatic notch and the posterior acetabular
rim). Osteotomy hinges at the triradiate cartilage
posteriorly and the symphysis pubis anteriorly. This
osteotomy does do not enter the sciatic notch and is
therefore stable and does not need internal
fixation. Reduces acetabular volume
Dega Favored in
neuromuscular
dislocations (CP) and
patients with posterior
acetabular deficiency; for
severe cases
Osteotomy from acetabular roof to triradiate cartilage
(incomplete cuts through pericapsular portion of the
innominate bone). The acetabular configuration changes
by hinging through the triradiate cartilage. This
osteotomy does do not enter sciatic notch and is therefore
stable and does not need internal fixation. Reduces the
acetabular volume
Dial Technically difficult and
rarely used
The dial or spherical osteotomy leaves the medial wall
or teardrop in its original position and, as a result, is intra-
articular.
Nursing Care Management
Nurses are in a unique position to detect DDH in early infancy. During the infant assessment
process and routine nurturing activities, the hips and extremities are inspected for any deviations
from normal. These observations are reported to the attending practitioner, and an ambulatory
child who displays a limp or an unusual gait should be referred for evaluation. This may indicate
an orthopedic or neurologic problem. Non ambulatory children with cerebral palsy should also
be assessed for evidence of hip problems. The major nursing problems in the care of an infant or
child in a cast or other device are related to maintenance of the device and adaptation of
nurturing activities to meet the patient’s needs. Generally, treatment and follow-up care of these
children are carried out in an outpatient setting.
The primary nursing goal is teaching parents to apply and maintain the reduction device.
The Pavlik harness allows for easy handling of the infant and usually produces less
apprehension in the parent than heavy braces and casts. Because of infants’ rapid growth,
the straps should be checked in the beginning of therapy and every 1 to 2 weeks for
adjustments .It is important that parents understand the correct use of the appliance,
which may or may not allow for its removal during bathing. Removing the harness is
determined individually on the basis of the provider’s recommendation, the family’s level
of understanding, and the degree of hip deformity. Parents are instructed to not adjust the
harness. The child should be examined by the practitioner before any adjustment is
attempted to make certain the hips are in correct placement.
Skin care is an important aspect of the care of an infant in a harness. The following instructions
for preventing skin breakdown are stressed:
• Always put an undershirt (or a shirt with extensions that close at the crotch) under the chest
straps and put knee socks under the foot and leg pieces to prevent the straps from rubbing the
skin.
• Check frequently (at least two or three times a day) for red areas under the straps and the
clothing.
17
• Gently massage healthy skin under the straps once a day to stimulate circulation. In general,
avoid lotions and powders because they can cake and irritate the skin.
• Always place the diaper under the straps. Parents are encouraged to hold the infant with a
harness and continue care and nurturing activities. The nurse can assist by being available for
parents’ questions about the necessary adaptations to daily care to decrease the parents’ anxiety
and possible feelings about the child being hurt by routine caring. Casts and orthotic devices
(braces) offer more challenging nursing and caregiver problems because they cannot be removed
for routine care, although sometimes a brace may be removed for bathing. Care of an infant or
small child with a cast requires nursing innovation to reduce irritation and to maintain cleanliness
of both the child and the cast, particularly in the diaper area. It is important for nurses, parents,
and other caregivers to understand that children in corrective devices need to be involved in all
of the activities of any child in the same age group. Confinement in a cast or appliance should
not exclude children from family (or unit) activities. They can be held astride the lap for comfort
and transported to areas of activity. The child may be allowed to walk in a cast or orthotic
device. An adapted wheelchair, stroller, or scooter can offer mobility to an older infant or child.
Nursing Care plan for DDH
• Pain relief
• protect operated joint from further injury
• RICE therapy (Rest, Ice, Compression, Elevation)
• Immobilization
• Family support
• Making sure that the family understand the rehabilitation program
• Demonstrating the adaptation required for patients in cast
18
• making sure that the family understand how to check for suture line infections and if
there are drainage or bad odor from the cast and the importance of reporting them immediately
Nursing diagnosis:
1. Impaired physical mobility R/T dislocation of hip, and presence of splint or cast
Interventions
1. Maintain the correct position of the hip.
2. Explain the components and purposes of splint or cast.
3. Enhance play and using the upper portion of the body.
4. Teach walking with cast
5. Support the casted limp and avoid pressure on heels
Nursing diagnosis:
2. Potential for injury, neurovascular impairment R/T compression by cast.
Interventions
1. Watch for signs of compression
2. Observe pedal pulse and ability to move fingers
3. Ask for tingling, numbness, pain, or burning sensation
4. Assess for tightness by inserting finger between cast and skin
19
Nursing diagnosis:
3. Knowledge deficit of parent regarding home care:
Interventions
1. Teach how to care of the child
2. Different treatment procedures
3. Involve parent in care of the child
4. Regular Follow up.
COMPLICATIONS
Numerous possible complications can occur, including re dislocation, stiffness of the hip,
infection, blood loss, and, possibly the most devastating, avascular necrosis of the femoral head.
The rate of femoral head necrosis varies substantially; depending on the study, it may be
anywhere from 0% to 73%. Numerous studies demonstrate that extreme abduction, especially
when combined with extension and internal rotation, results in a higher rate of avascular
necrosis.
PROGNOSIS
Overall, the prognosis for children treated for hip dysplasia is very good, especially if the
dysplasia is managed with closed treatment. If closed treatment is unsuccessful and open
reduction is needed, the outcome may be less favorable, although the short-term outcome
appears to be satisfactory. If secondary procedures are needed to obtain reduction, then the
overall outcome is significantly worse.
Some authors believe that patients with bilateral hip dysplasia have a poorer prognosis because
of frequent delays in diagnosis and greater treatment requirements. In a study comparing the
20
outcomes of walking-age children with bilateral hip dislocations who underwent open reduction
and pelvic osteotomy with or without femoral osteotomy with those of walking-age children with
unilateral dislocated hips who underwent the same set of procedures, the radiographic outcomes
were similar.
CLUB FOOT
Definition
Clubfoot is a complex deformity of the ankle and foot that includes forefoot adduction, midfoot
supination, hindfoot varus, and ankle equinus. Deformities of the foot and ankle are described
according to the position of the ankle and foot. The more common positions involve the
following variations:
Talipes varus—An inversion, or bending inward
Talipes valgus—An eversion, or bending outward
Talipes equinus—Plantar flexion, in which the toes are lower than the heel
Talipes calcaneus—Dorsiflexion, in which the toes are higher than the heel
Talipes equinovarus—Toes lower than the heel and facing inward
21
EPIDEMIOLOGY
The incidence of clubfoot is approximately 1 case per 1000 live births in the United States. The
incidence differs among ethnicities. For example, it is close to 75 cases per 1000 live births in
the Polynesian islands, particularly in Tonga.
The male-to-female ratio is 2:1. Bilateral involvement is found in 30-50% of cases. There is a
10% chance of a subsequent child being affected if the parents already have a child with a
clubfoot.
Parker et al pooled data from several birth defects surveillance programs (6139 cases of clubfoot)
to better estimate the prevalence of clubfoot and investigate its risk factors. The overall
prevalence of clubfoot was 1.29 per 1,000 livebirths, with 1.38 among non-Hispanic whites, 1.30
among Hispanics, and 1.14 among non-Hispanic blacks or African Americans. Maternal age,
22
parity, education, and marital status were significantly associated with clubfoot, along with
maternal smoking and diabetes.
CLASSIFICATION
Clubfoot may be further divided into three categories:
(1) Positional clubfoot (also called transitional, mild, or postural clubfoot), which is believed to
occur primarily from intrauterine crowding and responds to simple stretching and casting;
(2) Syndromic (or teratologic) clubfoot, which is associated with other congenital anomalies
such as myelomeningocele or arthrogryposis and is a more severe form of clubfoot that is often
resistant to treatment;
(3) Congenital clubfoot, also referred to as idiopathic, which may occur in an otherwise normal
child and has a wide range of rigidity and prognosis. The mild, or postural, clubfoot may correct
spontaneously or may require passive exercise or serial casting. There is no bony abnormality,
but there may be tightness and shortening of the soft tissues medially and posteriorly. The
teratologic clubfoot usually requires surgical correction and has a high incidence of recurrence.
The congenital idiopathic clubfoot, or “true clubfoot,” almost always requires surgical
intervention because there is bony abnormality
ETIOLOGY
The true etiology of congenital clubfoot is unknown. Most infants who have clubfoot have no
identifiable genetic, syndromal, or extrinsic cause.
Extrinsic associations include teratogenic agents (eg, sodium aminopterin),oligohydramnios, and
congenital constriction rings. Genetic associations include mendelian inheritance (eg, diastrophic
dwarfism; autosomal recessive pattern of clubfoot inheritance).
Cytogenetic abnormalities (eg, congenital talipes equinovarus [CTEV]) can be seen in
syndromes involving chromosomal deletion. It has been proposed that idiopathic CTEV in
otherwise healthy infants is the result of a multifactorial system of inheritance. Evidence for this
is as follows:
23
• Incidence in the general population is 1 per 1000 live births
• Incidence in first-degree relations is approximately 2%
• Incidence in second-degree relations is approximately 0.6%
• If one monozygotic twin has a CTEV, the second twin has only a 32% chance of having a
CTEV
Factors related to bone anatomy include the following:
Tibia - Slight shortening is possible
Fibula - Shortening is common
Talus - In equinus in the ankle mortise, with the body of the talus being in external rotation, the
body of the talus is extruded anterolaterally and is uncovered and can be palpated; the neck of
the talus is medially deviated and plantarflexed; all relations of the talus to the surrounding
bones are abnormal
Os calcis - Medial rotation and an equinus and adduction deformity are present
Navicular - The navicular is medially subluxated over the talar head
Cuboid - The cuboid is medially subluxated over the calcaneal head
Forefoot - The forefoot is adducted and supinated; severe cases also have cavus with a dropped
first metatarsal
Factors related to muscle anatomy include the following:
Atrophy of the leg muscles, especially in the peroneal group, is seen in clubfeet
The number of fibers in the muscles is normal, but the fibers are smaller
The triceps surae, tibialis posterior, flexor digitorum longus (FDL), and flexor hallucis longus
(FHL) are contracted
The calf is smaller and remains so throughout life, even after successful long-lasting correction
of the feet
Thickening of the tendon sheaths frequently is present, especially of the tibialis posterior and
peroneal sheaths. Contractures of the posterior ankle capsule, subtalar capsule, and talonavicular
and calcaneocuboid joint capsules commonly are seen. Contractures are seen in the
calcaneofibular, talofibular, (ankle) deltoid, long and short plantar, spring, and bifurcate
ligaments. The plantar fascial contracture contributes to the cavus, as does contracture of fascial
planes in the foot.
24
PATHOPHYSIOLOGY
Various theories of the pathogenesis of clubfeet have been advanced, including the following:
Arrest of fetal development in the fibular stage
Defective cartilaginous anlage of the talus
Neurogenic factors
Retracting fibrosis
Anomalous tendon insertions
Seasonal variations
With respect to neurogenic factors, histochemical abnormalities have been found in
posteromedial and peroneal muscle groups of patients with clubfeet. This is postulated to be due
to innervation changes in intrauterine life secondary to a neurologic event, such as a stroke
leading to mild hemiparesis or paraparesis. This is further supported by a 35% incidence of varus
and equinovarus deformity in spina bifida.
Retracting fibrosis (or myofibrosis) may occur secondary to increased fibrous tissue in muscles
and ligaments. In fetal and cadaveric studies, Ponseti also found the collagen in all of the
ligamentous and tendinous structures (except the Achilles [calcaneal] tendon), and it was very
loosely crimped and could be stretched. The Achilles tendon, on the other hand, was made up of
tightly crimped collagen and was resistant to stretching. Zimny et al found myoblasts in medial
fascia on electron microscopy and postulated that they cause medial contracture.
Inclan proposed that anomalous tendon insertions result in clubfeet. However, other studies have
not supported this proposal. It is more likely that the distorted clubfoot anatomy can make it
appear that tendon insertions are anomalous.
Robertson noted seasonal variations to be a factor in his epidemiologic studies in developing
countries. This coincided with a similar variation in the incidence of poliomyelitis in the children
in the community. Clubfoot was therefore proposed to be a sequela of a prenatal poliolike
condition. This theory is further supported by motor neuron changes in the anterior horn in the
spinal cord of these babies.
25
DIAGNOSTIC EVALUATION
Seek a detailed family history of clubfoot or neuromuscular disorders, and perform a general
examination to identify any other abnormalities. Examine the feet with the child prone, with the
plantar aspect of the feet visualized and supine to evaluate internal rotation and varus. If the child
can stand, determine whether the foot is plantigrade, whether the heel is bearing weight, and
whether it is in varus, valgus, or neutral.
Imaging Studies
Imaging studies generally are not required to understand the nature or the severity of the
deformity. Radiography, however, provides a useful baseline before and after surgical correction
of the feet, closed Achilles tenotomy, or a limited posterior release. Radiographs show the true
gain in foot (ankle) dorsiflexion and confirm the appearance of an iatrogenic rockerbottom foot
should one result. Occasionally, radiographs are necessary to diagnose clubfeet associated with
tibial hemimelias.
THERAPEUTIC MANAGEMENT
Medical Therapy
The aims of medical therapy for clubfoot are to correct the deformity early and fully and to
maintain the correction until growth stops.
Traditionally, two categories of clubfeet are identified, as follows:
• Easy or correctable clubfeet - These are readily corrected with manipulation, casting, and
splintage alone
• Resistant clubfeet - These respond poorly to splinting and relapse quickly after seemingly
successful manipulative treatment; they require early operative management and are said to be
associated with a thin calf and a small high heel.
The Pirani scoring system, devised by Shafiq Pirani, MD, of Vancouver, BC, consists of six
categories, three in the hindfoot and three in the midfoot, as follows:
• Curvature of the lateral border (CLB) of the foot
26
• Medial crease (MC)
• Uncovering of the lateral head of the talus (LHT)
• Posterior crease (PC)
• Emptiness of the heel (EH)
• Degree of dorsiflexion (DF)
The first three (CLB, MC, and LHT) constitute the midfoot score, and the last three (PC, EH, and
DF) constitute the hindfoot score.Each category is scored as 0, 0.5, or 1. The lowest possible (ie,
best) total score for all categories combined is 0, and the highest possible (ie, worst) total score is
6. The Pirani scoring system can be used to identify the severity of the clubfoot and to monitor
the correction.
It is necessary to provide counsel and advice to parents. They should be reassured that they are in
no way responsible for the deformity and that it is unlikely to be reproduced in subsequent
pregnancies.
Traditional non operative treatment
With traditional non operative treatment, splintage begins at 2-3 days after birth. The order of
correction is as follows:
• Forefoot adduction
• Forefoot supination
• Equinus
Attempts to correct equinus first may break the foot, producing a rockerbottom foot . Force must
never be used. Merely bring the foot to the best position obtainable, and maintain this position
either by strapping every few days or by changing casting weekly until either full correction is
obtained or correction is halted by some irresistible force.
27
The corrected position is maintained for several months. Surgery should be used as soon as it is
obvious that conservative treatment is failing (persisting deformity, rockerbottom deformity, or
rapid relapse after correction has stopped).
By 6 weeks, it is usually apparent whether the foot is easy or resistant; this is confirmed on x-ray
due to the orientation of the bones. Reported success rates for these traditional casting methods
are 11-58%.
PONSETI METHOD
This method was developed by Ignacio Ponseti, MD, of the University of Iowa. The premise of
the method is based on Ponseti's cadaveric and clinical observations. A 2014 Cochrane review
found this approach to yield signficantly better results than either the Kite method or a traditional
approach, though it noted that the quality of the evidence was not high.
The Ponseti method may be divided into seven steps, as follows.
Step 1
The calcaneal internal rotation (adduction) coupled with plantarflexion is the key deformity. The
foot is adducted and plantarflexed at the subtalar joint, and the goal is to abduct the foot and
dorsiflex it. In order to achieve correction of the clubfoot, the calcaneum should be allowed to
rotate freely under the talus, which also is free to rotate in the ankle mortise.
The correction takes place through the normal arc of the subtalar joint. This is achieved by
placing the index finger of the operator on the medial malleolus to stabilize the leg and levering
on the thumb placed on the lateral aspect head of the talus while abducting the forefoot in
supination. Forcible attempts to correct the heel varus by abducting the forefoot while applying
counterpressure at the calcaneocuboid joint prevent the calcaneum from abducting and therefore
everting.
Step 2
Foot cavus increases when the forefoot is pronated. If cavus is present, the first step in the
manipulation process is to supinate the forefoot by gently lifting the dropped first metatarsal to
correct the cavus. Once the cavus is corrected, the forefoot can be abducted as outlined in step 1.
28
Step 3
Pronation of the foot also causes the calcaneum to jam under the talus. The calcaneum cannot
rotate and stays in varus. The cavus increases as outlined in step 2. This results in a bean-shaped
foot. At the end of step 1, the foot is maximally abducted but never pronated.
Step 4
The manipulation is carried out in the cast room, with the baby having been fed just before, or
even during, the treatment. After the foot is manipulated, a long leg cast is applied to hold the
correction.
Initially, the short leg component is applied. The cast should be snug with minimal but adequate
padding. The authors paint or spray the limb with tincture of benzoin to allow adherence of the
padding to the limb. The authors prefer to apply additional padding strips along the medial and
lateral borders to facilitate safe removal of the cast with a cast saw. The cast must incorporate the
toes right up to the tips but not squeeze the toes or obliterate the transverse arch. The cast is
molded to contour around the heel while abducting the forefoot against counter pressure on the
lateral aspect of the head of the talus.
The knee is flexed to 90° for the long leg component of the cast. The parents can soak these casts
for 30-45 minutes before removal with a plaster knife. The authors' preferred method is to use
the oscillating plaster saw for cast removal. The cast is bivalved and removed. The cast then is
reconstituted by coapting the two halves. This allows for monitoring of the progress of the
forefoot abduction and, in the later stages, the amount of dorsiflexion or equinus correction.
Step 5
Forcible correction of the equinus (and cavus) by dorsiflexion against a tight Achilles tendon
results in a spurious correction through a break in the midfoot, resulting in a rockerbottom foot.
The cavus should be separately treated as outlined in step 2, and the equinus should be corrected
without causing a midfoot break. It generally takes as many as four to seven casts to achieve
maximum foot abduction. The casts are changed weekly. The foot abduction (correction) can be
considered adequate when the thigh-foot axis is 60°.
29
After maximal foot abduction is obtained, most cases require a percutaneous Achilles tenotomy.
This is performed in the cast room under aseptic conditions. The local area is anesthetized with a
combination of a topical lidocaine preparation (eg, EMLA Cream; AstraZeneca, Wilmington,
DE) and minimal local infiltration of lidocaine. The tenotomy is performed through a stab
incision with a round-tip (#6400) Beaver blade.
The wound is closed with a single absorbable suture or with adhesive strips.The final cast is
applied with the foot in maximum dorsiflexion, and the foot is held in the cast for 2-3 weeks.
Step 6
After the manipulation and casting phase, the feet are fitted with open-toed straight-laced shoes
attached to a Dennis Brown bar. The affected foot is abducted (externally rotated) to 70° with the
unaffected foot set at 45° of abduction. The shoes also have a heel counter bumper to prevent the
heel from slipping out of the shoe. The shoes are worn for 23 hours a day for 3 months and are
worn at night and during naps for up to 3 years.
Step 7
In 10-30% of cases, a tibialis anterior tendon transfer to the lateral cuneiform is performed when
the child is approximately 3 years of age. This gives lasting correction of the forefoot, preventing
metatarsus adductus and foot inversion. This procedure is indicated in a child aged 2-2.5 years
with dynamic supination of the foot. Before surgery, cast the foot in a long leg cast for a few
weeks to regain the correction.
Surgical Therapy
Preparation for operation
The operating room is kept warm, and a general anesthetic is used. The usual position is supine
with the foot resting over the contralateral leg in a figure-four position. Some surgeons prefer the
lateral decubitus position or even a prone position. A tourniquet generally is used, and the
surgical procedure is performed with the help of optical loupe magnification.
Incision
Options for incisions include the following:
30
• Cincinnati incision
• Turco curvilinear medial or posteromedial incision
The Cincinnati incision is a transverse incision that extends from the anteromedial (region of
navicular-cuneiform joint) to the anterolateral (just distal and medial to the sinus tarsi) aspect of
the foot and over the back of the ankle at the level of the tibiotalar joint.
The Turco incision can lead to wound breakdowns, especially at the corner of the vertical and
medial limbs.To avoid this problem, some surgeons prefer to use either three separate incisions
(posterior vertical, medial, and lateral) or two separate incisions (curvilinear medial and
posterolateral).
Any approach should be able to address the release in all quadrants, as follows:
• Plantar - Plantar fascia, abductor hallucis, flexor digitorum brevis, long and short plantar
ligaments
• Medial - Medial structures, tendon sheaths, talonavicular and subtalar release, tibialis
posterior, flexor hallucis longus (FHL), and flexor digitorum longus (FDL) lengthening
• Posterior - Ankle and subtalar capsulotomy, especially releasing post talofibular and
tibiofibular ligaments and the calcaneofibular ligaments
• Lateral - Lateral structures, peroneal sheath, calcaneocuboid joint, and completion of
talonavicular and subtalar release
Surgical clubfoot release
In the past, clubfoot surgery was performed in a way that did not differentiate severity. The same
procedure was performed for all patients. Bensahel proposed a more individualized approach (ie,
addressing only the structures that are required are released). The surgery is tailored to the
deformity. For example, if the forefoot is well corrected and externally rotated, if there is no
cavus, but if there is still significant equinus, a posterior approach alone should suffice.
Any approach should afford adequate exposure. Structures to be released or lengthened are the
following:
31
• Achilles (calcaneal) tendon
• Tendon sheaths of the muscles crossing the subtalar joint
• Posterior ankle capsule and deltoid ligament
• Inferior tibiofibular ligament
• Fibulocalcaneal ligament
• Capsules of the talonavicular and subtalar joints
• Division of associated ligaments around the subtalar joint
• Plantar fascia and intrinsic muscles
The longitudinal axis of the talus and calcaneum should be separated by about 20° in the lateral
projection, and the calcaneal angle should be a right angle to the shaft of the tibia.
The correction is held with wires at the talocalcaneal joint, the talonavicular joint, or both,
possibly with a plaster cast. The wound should never be forcibly closed. It can be left open to
granulate and heal by secondary intention or even grafted with split-thickness skin grafts.
Surgical treatment should take into account the age of the patient, as follows:
• In children younger than 5 years, correction can be achieved with soft-tissue procedures
• Children older than 5 years require bony reshaping (eg, dorsolateral wedge excision of
the calcaneocuboid joint [Dillwyn Evans procedure] or osteotomy of the calcaneum to correct
varus)
• If the child is older than 10 years, lateral wedge tarsectomy or triple fusion (arthrodesis)
is required (salvage procedures)
Posterior release steps, in brief, are as follows:
• Longitudinal incision
• Z-lengthened tendocalcaneus
• Identify neurovascular (NV) bundle
32
• Tendon sheaths of FHL, FDL, and tibialis posterior released; tendons not elongated
• Ankle joint capsule opened; talofibular, calcaneofibular, and deep portion of deltoid
ligaments released (blunt dissection)
• Release of distal tibial and fibula ligaments
• Posterior release of the subtalar joint
• With foot held just above neutral, tendocalcaneum is repaired and skin closed
• Plaster-of-Paris cast in corrected position for 4 weeks, followed by splints until maturity
A posteromedial release (Turco procedure) is performed as follows.
Make a medial incision 8-9 cm long from the base of the first metatarsal to the tendocalcaneum,
curving it just inferior to the medial malleolus without undermining skin. Mobilize and expose
the tendons of the tibialis posterior, FDL, FHL, Achilles tendon, and posterior NV bundle.
Continuing the incision in the sheaths of FDL and FHL, divide the master knot of Henry beneath
the navicular. Divide the spring ligament, detaching it from the sustentaculum tali and the origin
of the abductor hallucis. Release the remaining contractures, starting posteriorly. Lengthen the
Achilles tendon (Z-plasty), detaching the medial half of the tendon insertion.
Retract the NV bundle and FHL anteriorly to expose the posterior aspect of the ankle and
subtalar joints. Then, incise the posterior capsule of the ankle joint under direct visualization, as
well as the posterior talofibular ligament (if necessary at this time). Divide the subtalar capsule
and calcaneofibular ligament.
Retract the NV bundle posteriorly, and divide the tibiocalcaneal part of the deltoid ligament.
Lengthen the tibialis posterior if it is contracted. Open the talonavicular joint and divide its
capsule, but avoid damaging the articular surface. Then, release the subtalar ligaments and
reduce the navicular onto the head of the talus, which should properly align the other tarsal
bones.
Ensure that the relation of the talus to the calcaneus and navicular is correct, and stabilize the
foot with Kirschner wires (K-wires). The first K-wire is passed from the dorsum of the foot
33
across the first metatarsal shaft, the medial cuneiform, the navicular, and into the talus. A second
wire fixes the subtalar joint, and this should maintain the foot in the corrected position.
Apply an above-the-knee plaster-of-Paris cast, which is changed at 3 weeks and maintained to 6
weeks. The foot is initially held in slight equinus if there is tension on the skin closure, which is
corrected at the time of cast change. Splintage is continued for at least 4 months after surgery,
and night splints are used for several years.
The Ilizarov correction is used for recurrent clubfeet, especially in conditions such as
arthrogryposis. The calcaneum is held with two opposing olive-tipped wires. The distractor
force, in the form of heel-pushing distractors, must be posteriorly directed to prevent anterior
subluxation of the talus in the ankle mortise.
Postoperative care
Pay meticulous attention to the wound after surgery. If the skin closure is difficult, it is better to
leave the wound open and allow it to granulate for a delayed primary or secondary closure or
allow it to heal by granulation tissue. Skin grafts also can be used to cover the defect. The plaster
splint should be only lightly applied, and the wound should be inspected regularly.
The transfixion pins usually are removed in 3-6 weeks. The foot requires splintage in appropriate
footwear for 6-12 months.
NURSING CARE MANAGEMENT
Nursing care of the child with clubfoot is the same as for any child who has a cast . Because the
child will spend considerable time in a corrective device, nursing care plans include both long-
and short term goals. Conscientious observation of the skin and circulation is particularly
important in young infants because of their rapid growth rate. Because treatment and follow-up
care are handled in the orthopedist’s office, clinic, or outpatient department, parent education and
support are important in nursing care of these children. It is important for parents to understand
the overall treatment program, the importance of regular cast changes, and the role they play in
the long-term effectiveness of the therapy. Reinforcing and clarifying the orthopedist’s
explanations and instructions, teaching parents about care of the cast or appliance (including
vigilant observation for potential problems), and encouraging parents to facilitate normal
34
development within the limitations imposed by the deformity or therapy are all part of nursing
responsibilities.
Nursing care Plan
• Nursing diagnosis 1: Risk for altered peripheral tissue perfusion R/T pressure from cast.
•Interventions
– Keep the casted extremity elevated to prevent edema.
– Check circulation frequently (Every 15 min for the first 1 h, hourly for 24 h and 4 hourly there
after.
– Assess for color, warmth, presence of pedal pulses and sensations of numbness or tingling.
– Signs of impaired neurovascular function are pain, pallor, pulselessness and parasthesia.
– Edema that is not improved by elevation indicates also neurovascular impairment.
• Nursing diagnosis 2: Risk for impaired tissue integrity R/T pressure from cast.
• Interventions
– When moving child in a wet cast, always use open palms to move the cast.
– Pressing with fingers indent the cast and cause pressure points which can lead to an ulcer.
– Turn the child every 2 h to allow the under surface of the cast to dry.
– Do not use heaters or fans to dry the cast as it causes uneven drying.
– When the cast is dry if the edges are not smooth or covered by a fold of stockinet smooth the
adges by applying adhesive tape strips (Petaling)
– If casted area covers the genitalia cover the edges of the cast covering the genital area with a
plastic or waterproof material.
– Keep the child in a semifowler’s position.
35
– Teach the child nothing to put between the cast and skin.
• Nursing diagnosis 3: Parental health seeking behaviors R/T care of child with cast at home.
• Interventions
– If the cast is for the lower extremity discuss how much weight bearing is allowed, and the use
of crutches if prescribed.
– Reassure the parents that the child is comfortable with the cast.
– Demonstrate how to move or position the child and allow return demonstrations.
– If an abduction bar is used with the cast the parents should not use it as a handle to move or lift
the child.
– Encourage providing touch stimulation to the remaining body parts.
– If itching is a problem instruct them to apply a hand lotion or massage the area gently if it is
reachable.
– If not reachable blow cool air through the cast using a fan.
– Instruct not to put any thing inside to scratch.
Teaching Plan- contents
• Physical care:
1. Maintain appropriate muscle tone
2. Provision of comfort
3. Traction/ Cast care
4. Prevention of urinary stasis and constipation
5. Promotion of skin integrity
• Parent teaching:
36
• How to apply devices such as Denis Brown splint.
• Explain the procedure
• Teaching of diversional therapy during application of traction/cast
• Caring of cast? (wet, how to dry)
• Assess for circulatory and neurological disturbance
COMPLICATIONS
Complications of treatment of clubfoot include the following:
• Infection (rare)
• Wound breakdown - Release skin retractors every 30 minutes, and release the tourniquet
before closing the wound and applying a cast
• Stiffness and restricted range of motion - Early stiffness correlates with a poor result
• Avascular necrosis (AVN) of the talus - A 40% incidence of avascular necrosis of the
talus occurs with combined simultaneous medial and lateral release
• Persistent intoeing - This is quite common; it is due not to tibial intorsion but, rather, to
insufficient external rotation correction of the subtalar joint
Overcorrection is associated with the following:
• Release of the interosseous ligament of the subtalar joint
• Excess lateral displacement of the navicular on the talus
• Overlengthening of tendon units
For residual deformity following the initial surgery, rule out neurologic causes of recurrence (eg,
tethered cord). A residual deformity may be either of the following:
• Dynamic - With residual adductus and supination that are fully correctable passively,
treat with split anterior tibial tendon transfer
37
• Fixed - If scarring is not excessive and the patient is younger than 5 years, repeat the
release; if the patient is older than 5 years, a bony procedure to straighten the lateral border of the
foot is required
Options to correct adductus are as follows:
• Metatarsal osteotomy - This operation creates a secondary deformity to compensate for a
primary deformity in the tarsus; it rarely is indicated
• Cuboid decancellation
• Calcaneocuboid fusion - The Dillwyn Evans procedure consists of a medial and post
release together with excision and fusion of the calcaneocuboid joint ; it should be reserved for
patients older than 4 years; these two procedures aim to shorten the lateral side of the foot
• Lengthening the medial side of the foot (eg, talar osteotomy) - This is not widely
performed; AVN is a risk
Options to correct residual hindfoot deformity are the following:
• Heel varus - Open the medial wedge, or close the lateral wedge; lateral displacement os
calcis osteotomy is preferred
• Residual cavus and adductus - Perform a wedge tarsectomy
• Failed feet - Perform a triple arthrodesis
PROGNOSIS
Approximately 50% of clubfeet in newborns can be corrected nonoperatively. Ponseti has
reported an 89% success rate using his technique (including an Achilles tenotomy); others have
reported success rates of 10-35%. One study analyzed the correction progression of patients with
idiopathic clubfeet after the Ponseti technique. The data indicated that successive castings
resulted in reduced cavus and medial crease with a gradual correction of midfoot rotation,
adduction, and heel varus. Interestingly, heel equinus improved concurrent with midfoot
variables and also with final casting.
CONCLUSION:
38
For children, one of the most difficult aspects of illness is immobilization. Throughout
childhood, physical activity is an integral part of daily life and is essential for physical growth
and development. It also serves children as an instrument for communication and expression and
as a means for learning about and understanding their world. Activity helps them deal with a
variety of feelings and impulses and provides a mechanism by which they can exert control over
inner tensions. Children respond to anxiety with increased activity. Removal of this power
deprives them of necessary input and a natural outlet for their feelings and fantasies. Through
movement, children also gain sensory input, which provides an essential element for developing
and maintaining body image. So correct care given at correct time can prevent immobility or
movement problems in children.
BIBLIOGRAPHY
John cloherty.P, Eric Eichenwald C, Annie, Hansen R. Manual of neonatal care. 7th
edition. South east asia: Lippincott Williams and Wilkins;2012.
Santosh Kumar .A. Manual of newborn care . 2nd edition. Newdelhi:Paras Medical
Publication; 2011.
Tauesch, Ballard, Gleason. Avery’s diseases of the new born. 8th edition. Philadelphia:
Elsevier Publication; 2005
DuttaD.C. Text book of Obstetrics.Culcutta.New central book agency: 2004
Marilyn Hocken berry,david Wilson.Wong’s Essentials of Pediatric Nrsing.9th
edition.Elsevier Publication.2009
Parthasarathy.Parthas Fundamentals of pediatrics.2nd edition.Newdelhi.Jaypee
Publicatio;2013
Dorothy.R.Marlow. Text Book of Pediatric Nursing.6th edition.Saunders
Publication;2007.
39