Diagnosis Banding Tumor Jaringan Lunak - Persentasi Referat
Transcript of Diagnosis Banding Tumor Jaringan Lunak - Persentasi Referat
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DIAGNOSIS BANDING
TUMOR JARINGAN
LUNAKPembimbing: dr. Ooki Nico Junior S! B"K#Onk
Ke!$ni%er$$n Bed$& RSUD 'i$(i
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KLASI)IKASI TUMOR JARINGAN
LUNAK* Adi!oc+c%ic Tumor Benign
Lipoma
Lipomatosis
Lipomatosis of nerve
Lipoblastoma / lipoblastomatosisAngiolipoma
Myolipoma of soft tissue
Chondroid lipoma
Extra-renal angiomyolipoma
Extra-adrenal myelolipoma
Spindle cell / pleomorphic lipoma
Hibernoma
Intermediate (localy aggressive)
Atypical lipomatous tumour / ell differentiated liposarcoma
Malignant
!edifferentiated liposarcoma
Myxoid liposarcoma
"leomorphic liposarcoma
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KLASI)IKASI TUMOR JARINGAN
LUNAK* )ibrob,$-%ic m+o/ibrob,$-%ic %umour-
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KLASI)IKASI TUMOR JARINGAN
LUNAK* )ibrob,$-%ic m+o/ibrob,$-%ic %umour-
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KLASI)IKASI TUMOR JARINGAN
LUNAK* So0c$,,ed /ibro&i-%ioc+%ic %umour-
* Smoo%&0mu-c,e %umour-
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KLASI)IKASI TUMOR JARINGAN
LUNAK* Peric+%ic "!eri1$-cu,$r# %umour-
* Ske,e%$,0mu-c,e %umour-
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KLASI)IKASI TUMOR JARINGAN
LUNAK* 2$-cu,$r %umour-
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KLASI)IKASI TUMOR JARINGAN
LUNAK* G$-%roin%e-%in$, -%rom$, %umour-
* Ner1e -&e$%& %umour-
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KLASI)IKASI TUMOR JARINGAN
LUNAK* Tumour- o/ uncer%$in di//eren%i$%ion
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KLASI)IKASI TUMOR JARINGAN
LUNAK* Tumour- o/ uncer%$in di//eren%i$%ion
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Adi!oc+%ic Tumour-
* Ke,om!ok %erbe-$r d$ri %umor me-enc&+m$, k$ren$
%inggin+$ !re1$,en-i ,i!om$ d$n $ngio,i!om$.
* Li!o-$rcom$ meru!$k$n -$rcom$ 3$ring$n ,un$k +$ng
!$,ing umum.
* Sec$r$ -ub%+!e 4i-%o,ogi- u%$m$n+$ beru!$ (e,,
di//eren%i$%ed m+5oid d$n !,eomor/ik -e!enu&n+$
memi-$&k$n !en+$ki% ini -ec$r$ mor/o,ogi +$ng berbed$
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Li!om$
De/ini-i
*%umor 3in$k +$ng %erdiri d$ri (&%e $di!oc+%e- m$%ur d$n
meru!$k$n %umor 3$ring$n ,un$k +$ng !$,ing -ering !$d$
or$ng de($-$.
6!idemio,ogi
*-ering !$d$ u-i$ 78 0 98 %$&un J$r$ng !$d$ $n$k0$n$k
*Obe-i%$-
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Li!om$
Si%e o/ in1o,1emen%
* 3$ring$n -ubku%$n ",i!om$ -u!er/i-i$,#
* 3$ring$n ,un$k d$,$m "dee! -e$%ed ,i!om$#
Li!om$ in%r$mu-ku,$ri- "b$%$ng %ubu& ke!$,$ d$n ,e&er b$gi$n$%$- d$n ek-%remi%$- b$($
Li!om$ in%ermu-ku,$ri- "dinding $bdomen#
*!ermuk$$n %u,$ng "P$ro-%e$, ,i!om$#
*
Li!om$ $rbore-cen-. "S+no1i$, ,i!om$#
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Li!om$
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Li!om$
M$ni-/e-%$-i K,ini-
*M$--$ 3$ring$n ,un$k %$n!$ di-er%$i n+eri "kec ,i!om$
ukur$n be-$r +$ng mengen$i -$r$/ !eri/er#
*Pembengk$k$n -endi " Li!om$ $rbore-cen-#
M$kro-ko!i
*berb$%$- %eg$-
*Ukur$n ; cm ",i!om$ -u!er/i-i$,#
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Li!om$
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Li!om$%o-i-
Per%umbu&$n ber,ebi& di/u- 3$ring$n $di!o-$ m$%ur
6!idemio,ogi
*bi$-$n+$ %imbu, !$d$ umur dib$($& = %$&un "Li!om$%o-i- di/u-#
*,$ki0,$ki berku,i% &i%$m di ki-$r$n umur >0?8 %$&un."Li!om$%o-i-!e,1ik#
*!er%eng$&$n umur !$d$ ,$ki0,$ki medi%er$ni$n deng$n ri($+$%!en+$ki% &$%i $kib$% kon-um-i $,ko&o, ber,ebi&$n."Li!om$%o-i--ime%rik#
*%er$!i &ormon$, $%$u !eningk$%$n !roduk-i $drenokor%ik$, -%eroid "Li!om$%o-i- -%eroid#
*Ter$!i !ro%e$-e in&ibi%or !$d$ or$ng AIDS d$n %er$!i$n%ire%ro1ir$, "4I20,i!odi-%ro/i#
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Li!om$%o-i-
Si%e- o/ In1o,1emen%
*Li!om$%o-i- di/u- "ke%erk$i%$n deng$n m$crod$c%+,+
gig$n%i-me# : b$%$ng %ubu& -eb$gi$n be-$r ek-%remi%$-
ke!$,$ d$n ,e&er !eru% !$nggu, $%$u 3$,ur in%e-%in$,
*Li!om$%o-i- -ime%rik : de!o-i-i -ime%ri- ,em$k di $%$-
b$gi$n %ubu& %eru%$m$ ,e&er.
*,i!om$%o-i- !$nggu,: d$er$& !eri1e-ic$, d$n !erirec%$,.
*Li!om$%o-i- -%eroid : ($3$& d$er$& -%ernum $%$u!unggung "Bu//$,o &um!#.
*4I20,i!odi-%ro/i : $kumu,$-i d$ri ,em$k 1i-cer$, $di!o-i%
!$+ud$r$ -er1ik- ($3$& d$n $nggo%$ b$d$n.
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Li!om$%o-i-
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Li!om$%o-i-
M$ni/e-%$-i k,ini-
*Neuro!$%i
*Ob-%ruk-i ,$ring
*Kom!re-i d$ri 1en$ c$1$*Menge,u& -$$% berkemi&
*N+eri !$d$ !erineum
*Sembe,i%
*N+eri !$d$ $bdomen d$n !unggung
*Ob-%ruk-i u-u-
*4idrone/ro-i-
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Li!om$%o-i-
M$kro-ko!i
*Le-i b$%$- kur$ng %eg$- deng$n $greg$% ,em$k ber($rn$
kuning ,embu% +$ng iden%ik deng$n !en$m!i,$n norm$,
,em$k.
*S$%u0-$%un+$ !erbed$$n $d$,$& ,ok$-i ke%er,ib$%$n d$n
di-%ribu-i ,em$k.
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A%+!ic$, %umor ,i!om$%ou- "ALT#
(e,,di//eren%i$%ed "@D# Li!o-$rkom$De/ini-i*neo!,$-m$ me-enc&+m$, g$n$- +$ng %erdiri -eb$gi$n$%$u -e!enu&n+$ !ro,i/er$-i $di!oc+%ic m$%ur +$ngmenun3ukk$n 1$ri$-i -igni/ik$n d$,$m ukur$n -e, d$n
-e%id$kn+$ $k%i!ik nuk,e$r /oc$, di kedu$ $di!o-i% d$n-%rom$ -e,.
6!idemio,ogi
*7807; d$ri -emu$ ,i!o-$rkom$*!erb$nding$n !ri$ d$n !erem!u$n -$m$
*%er3$di !$d$ !$ru& b$+$ de($-$ !unc$kn+$ dek$de ke 9
*L$ngk$ !$d$ $n$k0$n$k
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A%+!ic$, %umor ,i!om$%ou- "ALT#
(e,,di//eren%i$%ed "@D# Li!o-$rkom$Si%e o/ in1o,1emen%*-ering %er3$di !$d$ 3$ring$n ,un$k d$,$m $nggo%$ b$d$n
%eru%$m$ !$&$ diiku%i o,e& re%ro!eri%oneum d$er$&
!$r$%e-%iku,$r d$n medi$-%inum
*D$!$% %imbu, did$er$& -ubku%$n
*S$ng$% 3$r$ng !$d$ ku,i%
M$ni/e-%$-i k,ini-
*m$--$ +$ng membe-$r %$n!$ r$-$ -$ki% +$ng !er,$&$n0,$&$n bi-$ menc$!$i ukur$n +$ng -$ng$% be-$r
$-im!%om$%ik. "!$d$ re%ro!eri%oneum d$!$% menc$!$i
di$me%er =8cm#
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A%+!ic$, %umor ,i!om$%ou- "ALT#
(e,,di//eren%i$%ed "@D# Li!o-$rkom$M$kro-ko!i*m$--$ be-$r ber,obu- d$n berb$%$- %eg$-
*m$--$ mu,%i!,e +$ng -$,ing %id$k ber&ubung$n. "bi$-$n+$
!$d$ re%ro!eri%oneum# .*@$rn$ ber1$ri$-i d$ri ($rn$ kuning -$m!$i !u%i&
* Are$ nekro-i- ,em$k -ering di%emuk$n !$d$ ,e-i +$ng ,ebi&
be-$r.
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Nodu,$r )$cii%i-
De/ini-i
*m$--$ +$ng %erben%uk d$ri !ro,i/er$-i /ibro-$ +$ngbi$-$n+$ %er3$di !$d$ 3$ring$n -ubku%$n.
6!idemio,ogi
*-emu$ ke,om!ok umur %$!i ,ebi& b$n+$k -ering !$d$or$ng de($-$ mud$.
*in%r$1$-ku,$r /$-cii%i- d$n /$-cii%i- kr$ni$, 3$r$ng %er3$di.
*In%r$1$-ku,$r /$-cii%i- di%emuk$n keb$n+$k$n !$d$ or$ngdi b$($& 8 %$&un
*)$-cii%i- kr$ni$, berkemb$ng %eru%$m$ !$d$ b$+i di b$($&u-i$ = %$&un d$n ,ebi& -ering !$d$ $n$k ,$ki0,$ki
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Nodu,$r )$cii%i-
Si%e o/ In1o,1emen%
*Subku%$n me-ki!un %erk$d$ng in%r$mu-ku,$r.
*,ok$-i !$d$ ku,i% -$ng$% 3$r$ng.
*Sering !$d$ ek-%remi%$- $%$- b$%$ng %ubu&ke!$,$ d$n,e&er
*in%r$1$-ku,$r /$-cii%i- 3ug$ -ubku%$n. %er3$di !$d$
!embu,u& d$r$& keci, &ingg$ -ed$ng
*Kr$ni$, /$-cii%i- bi$-$n+$ me,ib$%k$n b$gi$n ,u$r d$ri%engkor$k d$n 3$ring$n ,un$k +$ng berdek$%$n d$ri ku,i%
ke!$,$ d$n d$!$% men3$,$r ke b$($& me,$,ui ,$!i-$n
b$gi$n d$,$m ke meningen-.
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Nodu,$r )$cii%i-
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M+o-i%i- o--i/ic$n- d$n /ibroo--eou-
!-eudo%umour o/ digi%-M+o-i%i- o--i/ic$n- "MO# d$n !-eudo%umor /ibroo--eou-digi% ")P# %er,ok$,i-ir -e,/ ,imi%ing ,e-i re!$r$%i/ +$ng %erdirid$ri re$k-i &i!er-e,u,er 3$ring$n /ibro-$ d$n %u,$ng.
6!idemio,ogi*u-i$ +$ng ,u$- mu,$i d$ri b$+i -$m!$i $k&ir de($-$ "C70>; %$&un#
*de($-$ mud$ "u-i$ r$%$0r$%$ = %$&un#
* 3$r$ng %er3$di !$d$ b$+i $%$u or$ng %u$*Pri$ ,ebi& b$n+$k d$ri!$d$ !erem!u$n ": =#
*!erem!u$n ,ebi& b$n+$k %er,ib$% di )P.
*P$-ien deng$n MO bi$-$n+$ $k%i/ -ec$r$ /i-ik.
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M+o-i%i- o--i/ic$n- d$n /ibroo--eou-
!-eudo%umour o/ digi%-Si%e o/ In1o,1emen%*MO berkemb$ng di ,ok$-i +$ng !$,ing ren%$n %er&$d$!
%r$um$ -e!er%i -iku !$&$ !$n%$% d$n b$&u.
*
)P bi$-$n+$ mem!eng$ru&i 3$ring$n -ubku%$n !rok-im$,!&$,$n5 3$ri %$ng$n d$n 3$r$ng di 3$ri03$ri k$ki.
M$ni/e-%$-i k,ini-
*Bengk$k d$n N+eri "C0= minggu#
*=09 minggu n+eri meng&i,$ng
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M+o-i%i- o--i/ic$n- d$n /ibroo--eou-
!-eudo%umour o/ digi%-M$kro-ko!i*m$--$ o1$, ber($rn$
cok,$% deng$n !u-$%
berki,$u ,embu% d$ndeng$n !inggir$n $bu0
$bu0!u%i& ber!$-ir
*ker$-
*Le-i berukur$n =0C= cm
"keb$n+$k$n -eki%$r ;
cm#.
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M+o-i%i- o--i/ic$n- d$n /ibroo--eou-
!-eudo%umour o/ digi%-
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M+5o/ibro-$rcom$
%erdiri -!ek%rum d$ri ,e-i /ibrob,$-%ik g$n$- deng$n 1$ri$be,
-%rom$ m+5oid !,eomor/i-me d$n deng$n !o,$ !embu,u&
d$r$& me,engkung +$ng k&$-.
6!idemio,ogi
*-$rkom$ +$ng !$,ing -ering !$d$ !$-ien u-i$ ,$n3u%
deng$n domin$-i -ediki% ,$ki0,$ki
*
Sering !$d$ dek$de keen$m -$m!$i kede,$!$n*S$ng$% 3$r$ng %er3$di di b$($& u-i$ =8 %$&un.
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M+5o/ibro-$rcom$
Si%e o/ In1o,1emen%
*gird,e ek-%remi%+ "rend$&< ek-%remi%$- $%$-#
*J$r$ng !$d$ b$%$ng %ubu& di ke!$,$ d$n d$er$& ,e&er
Re%ro!eri%oneum d$n rongg$ !eru% .
M$ni/e-%$-i k,ini-
*M$--$ +$ng !er,$&$n mem!erbe-$r
*N+eri
*kek$mbu&$n -ering beru,$ng* Neo!,$-m$ ke,$- %inggi neo!,$-m$ d$!$% berme%$-%$-i-
ke !$ru d$n %u,$ng
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M+5o/ibro-$rcom$
M$kro-ko!i
*Neo!,$-m$ %er,e%$k di !ermuk$$n bi$-$n+$ %erdiri d$ri
beber$!$ ber1$ri$-i ken+$, $%$u nodu, ,ebi& ker$-
Neo!,$-m$ !$d$ ,$!i-$n ,ebi& d$,$m -ering memben%uk
-u$%u m$--$ %ungg$, deng$n m$rgin in/i,%r$%i/.
*Neo!,$-m$ ke,$- %inggi -ering di%emuk$n d$er$& nekro-i-
%umor.
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M+5o/ibro-$rcom$
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Leiom+om$ o/ dee! -o/% %i--ue
Leiomiom$ +$ng %er3$di !$d$ 3$ring$n ,un$k d$,$m -om$%ik $%$ure%ro!eri%oneum rongg$ !eru% d$n meru!$k$n 3eni- %umor +$ng-$ng$% ,$ngk$.
6!idemio,ogi*,$ki0,$ki d$n !erem!u$n mem!un+$i !erb$nding$n r$-io +$ng-$m$
*ke,om!ok de($-$ mud$ $%$u !$ru& b$+$
Si%e o/ In1o,1emen%*6k-%remi%$- Re%ro!eri%oneum
*Pe,1i-
*Rongg$ !eru% " me-en%er+ d$n omen%um#
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Leiom+om$ o/ dee! -o/% %i--ue
M$kro-ko!i
*%umor berb$%$- %eg$-
*ber($rn$ $bu0$bu !u%i&.
*Di$me%er ,eiom+om$ d$ri 3$ring$n ,un$k -om$%ik d$,$mberki-$r =;0C; cm "r$%$0r$%$ cm# d$n +$ng !$,ing
-ering berukur$n ; cm $%$u ,ebi&
*ber$% %umor berki-$r =?0;788 g "r$%$0r$%$ C.988 g#
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Leiom+o-$rkom$
Tumor g$n$- %erdiri d$ri -e,0-e, +$ng berbed$ -e, o%o%!o,o-
6!idemio,ogi
*%er3$di !$d$ !$ru& b$+$ $%$u ,ebi& %u$ "d$!$% berkemb$ng!$d$ or$ng de($-$ mud$ d$n $n$k0$n$k#
Si%e o/ In1o,1emen%
*Re%ro!eri%oneum*Pe,1ik
*Pembu,u& d$r$& be-$r "umumn+$ 1en$ c$1$ in/erior d$n1en$ be-$r ek-%remi%$- b$($.
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Leiom+o-$rkom$
M$ni/e-%$-i k,ini-
*N+eri
*Sindrom Budd '&i$ri "&e!$%omeg$,i 3$undice d$n $-ci%e-#
*di-/ung-i gin3$,*edem$ k$ki
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Leim+o-$rcom$
M$kro-ko!i
m$--$ berd$ging
($rn$ ber1$ri$-i d$ri $bu0$bu men3$di !u%i& -$m!$i
coke,$%.
%$m!$k me,ingk$r !$d$ beber$!$ der$3$%.
E$ng ,ebi& be-$r -ering %$m!$k !erd$r$&$n nekro-i- $%$u
!erub$&$n ki-%ik.
%umor berb$%$- %eg$- deng$n b$ik
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Leim+o-$rcom$
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M+o!eric+%om$
M$ni/e-%$-i k,ini-
*nodu, -o,i%er %$n!$ n+eri -ediki% n+eri
*%umbu& ,$mb$% d$n d$!$% %imbu, -e,$m$ ber%$&un0%$&un
M$kro-ko!i
*nodu, +$ng cenderung berb$%$- %eg$- deng$n di$m$%er
berukur$n kur$ng d$ri = cm.
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M+o!eric+%om$
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Angio,eiom+om$
M$kro-ko!i
*nodu, berb$%$- %eg$-
*bu,$%
* $bu0$bu !u%i& $%$u cok,$%.*Fu$de nodu,
*Di$me%er kur$ng d$ri = cm.
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R&$bdom+om$
* %umor me-enc&+m$, 3in$k !$d$ o%o% r$ngk$.
Dik,$-i/ik$-ik$n men3$di = berd$-$rk$n %em!$%:
*RM c$rdi$k
* RM 6k-%r$c$rdi$k "RM !$d$ de($-$ d$n 3$nin#
* RM geni%$,
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Adu,% R&$bdom+om$
Tumor 3in$k me-enc&+m$, ,$ngk$ !$d$ di/eren-i$-i o%o%
r$ngk$ m$%ur d$n %imbu, !$d$ d$er$& ke!$,$ d$n ,e&er.
6!idemio,ogi
U-i$ r$%$0r$%$ $d$,$& 98 %$&un "ki-$r$n -$m!$i ?8
%$&un# deng$n !erb$nding$n : C domin$-i ,$ki0,$ki
Si%e o/ in1o,1emen%*muko-$ $erodige-%i1e "/$ring mu,u% rongg$ d$n ,$ring#
* 3$ring$n ,un$k ,e&er
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Adu,% R&$bdom+om$
M$ni/e-%$-i k,ini-
*ob-%ruk-i -$,ur$n n$!$- $%$- d$n m$--$ !$d$ muko-$
$%$u 3$ring$n ,un$k
M$kro-ko!i
*M$--$
*ukur$n cm "ki-$r$n C;0; cm#
*berb$%$- %eg$-*ber($rn$ cok,$% -$m!$i mer$&0cok,$%
*Lembu%
*bernodu, $%$u ber,obu-.
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Adu,% R&$bdom+om$
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52/70
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53/70
)e%$, R&$bdom+om$
M$ni/e-%$-i k,ini-
*m$--$ %ungg$, +$ng me,ib$%k$n 3$ring$n ,un$k $%$u
muko-$ "dur$-i r$%$0r$%$ ? bu,$n 3$r$k &$ri -$m!$i C>
%$&un#
M$kro-ko!i
*m$--$ %ungg$,
*berb$%$- %eg$-*,un$k
*ber($rn$ $bu0$bu !u%i& -$m!$i coke,$%0mer$& mud$
deng$n !o%ong$n !ermuk$$n berki,$u.
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54/70
)e%$, R&$bdom+om$
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55/70
Geni%$, R&$bdom+om$
Tumor me-enc&+m$, 3in$k ,$ngk$ deng$n %ingk$% di/eren-i$-i
o%o% r$ngk$ ,$n3u%$n d$n deng$n !redi,ek-i !$d$ 2$gin$
6!idemio,ogi
*&$m!ir -ec$r$ ek-k,u-i/ di !er%eng$&$n u-i$ !erem!u$n. .
*U-i$ r$%$0r$%$ $d$,$& 7= %$&un "ki-$r$n 807? %$&un#.
Si%e o/ in1o,1emen%*1$gin$
*1u,1$ $%$u
*,e&er r$&im.
*!$r$%e-%icu,$r $%$u e!ididimi- ." !$d$ ,$ki0,$ki 3$r$ng#
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Geni%$, R&$bdom+om$
M$ni/e-%$-i k,ini-
* M$--$ mungkin $-im%om$%ik $%$u %imbu, -$m!$i 70;
%$&un .
M$kro-ko!i
*M$--$ 1$gin$ !o,+!oid "ukur$n r$%$0r$%$ = cm ki-$r$n C0
cm#
*di%u%u!i o,e& muko-$ &$,u-.
*berb$%$- %eg$-
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S+no1i$, 4em$ngiom$
%umor !embu,u& d$r$& !ro,i/er$-i 3in$k +$ng %imbu, d$,$m
!ermuk$$n ,$!i-$n -ino1ium %erm$-uk ru$ng in%r$0$r%iku,$r
d$n bur-$
6!idemio,ogi
*S$ng$% 3$r$ng
*Keb$n+$k$n !$-ien $n$k $n$k $%$u rem$3$ d$n $d$
kecenderung$n un%uk ,$ki0,$ki.
Si%e o/ In1o,1emen%
*,u%u% diiku%i ,ebi& 3$r$ng o,e& -iku d$n %$ng$n.
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S+no1i$, 4em$ngiom$
M$ni/e-%$-i k,ini-
*,e-i +$ng %umbu& !er,$&$n
*!embengk$k$n d$n e/u-i
*N+eri beru,$ng
M$kro-ko!i
* %umor berb$%$- %eg$- d$n di/u-.
*Konge-%i d$n di,$%$-i !embu,u& d$r$&
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2enou- 4em$ngiom$
%erdiri 1en$ ukur$n 1$ri$be, -ering memi,iki dinding o%o%
%eb$,. in%r$mu-ku,$r $ngiom$ d$n $ngiom$%o-i- &$m!ir
d$!$% %er-u-un -ec$r$ ek-k,u-i/ d$ri 1en$ %$!i bi$-$n+$
berc$m!ur deng$n !embu,u& ,$in.
6!idemio,ogi
*24 3$r$ng d$n %imbu, %eru%$m$ !$d$ or$ng de($-$.
Si%e o/ in1o,1emen%
*-ubku%$n $%$u 3$ring$n ,un$k +$ng ,ebi& d$,$m d$n
cenderung !$d$ ek-%remi%$-.
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60/70
2enou- 4em$ngiom$
M$ni/e-%$-i k,ini-*%umor +$ng %umbu& !er,$&$n d$n0ber,$ng-ung ,$m$
M$kro-ko!i
*%umor berb$%$- %id$k %eg$- d$n
*%erdiri d$ri di,$%$-i
ru$ng 1$-ku,$r meng$,$mi konge-%i
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61/70
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Ar%erio1enou- 4em$ngiom$
M$ni/e-%$-i k,ini-
N+eri
&i!er%ro/i ek-%remi%$-
g$g$, 3$n%ungKo$gu,o!$%i "K$-$b$c&0Merri%% -+ndrome#.
M$kro-ko!i
B$%$- %umor %id$k %eg$- d$n meng$ndung 3um,$&!embu,u& d$r$& keci, d$n be-$r +$ng di,$%$-i
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63/70
Ar%erio1enou- 4em$ngiom$
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64/70
L+m!&$ngiom$
Le-i k$1erno-$ ki-%ik 1$-ku,$r 3in$k +$ng %erdiri d$ri di,$%$-i-$,ur$n ,im/$%ik. Beber$!$ k$-u- d$!$% diiden%i/ik$-i d$,$m
Sindrom %urner "d$n -indrom m$,/orm$%i/ ,$inn+$# d$n d$!$%
di%emuk$n d$,$m $bor%u-.
6!idemio,ogi
$n$k d$n -ering %imbu, !$d$ -$$% ,$&ir $%$u -e,$m$ %$&un
!er%$m$ ke&idu!$n.
Si%e o/ in1o,1emen%
*,e&er ke%i$k d$n -e,$ngk$ng$n ",+m!&$ngiom$ ki-%ik#
*rongg$ mu,u% b$%$ng %ubu& $%$- %ungk$i d$n !eru% %erm$-uk
me-en%erium d$n re%ro!eri%oneum ",+m!&$ngiom$ k$1erno-um#
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L+m!&$ngiom$
M$ni/e-%$-i k,ini-
!embengk$k$n %$n!$ r$-$ -$ki%
M$kro-ko!i
*m$--$ mu,%iki-%ik $%$u -!on- rongg$
*meng$ndung c$ir$n +$ng ber$ir -$m!$i -e!er%i -u-u. "($%er+ %o
mi,k+ /,uid#.
*,un$k d$n ber/,uk%u$-i !$d$ -$$% di !$,!$-i d$n bi-$
menun3ukk$n !er!ind$&$n org$n -eki%$rn+$ !$d$ d$er$&medi$-%inum $%$u in%r$$bdomin$,
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66/70
L+m!&$ngiom$
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67/70
S$rkom$ K$!o-i
Tumor endo%e, +$ng bi$-$n+$ %imbu, deng$n ,e-i ku,i%
beru!$ berc$k mu,%i!e, !,$k $%$u nodu, %e%$!i 3ug$ d$!$%
me,ib$%k$n muko-$ ke,en3$r ge%$& bening d$n org$n
1i-cer$,.
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69/70
S$rkom$ K$!o-i
M$kro-ko!i*Le-i !$d$ ku,i% "berc$k !,$k nodu,# ber1$ri$-i d$,$m
ukur$n d$ri +$ng -$ng$% keci, &ingg$ beber$!$ -en%ime%er
di$me%ern+$.
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70/70