D o r v

7
Double Outlet Right Ventricle (DORV)

Transcript of D o r v

Page 1: D o r v

Double Outlet Right Ventricle (DORV)

Page 2: D o r v

Double Outlet Right Ventricle (DORV)

DORV is a congenital heart defect in which both the aorta and pulmonary artery exit from the right ventricle. No arteries arise from the LV.

Aorta carries deoxygenated blood from the RV to the various parts of the body

DORV includes a VSD, pulmonary stenosis or TGA may also be part of the defect

Page 3: D o r v

Types

DORV occurs in multiple forms, with variability of great artery position and size as well as of VSD location.

The clinical manifestations are similarly variable, depending on how the anatomical defects affect the physiology of the heart, in terms of altering the normal flow of blood from the RV and LV to the aorta & pulmonary artery.

Page 4: D o r v

In DORV with a subaortic VSD, blood from the LV flows through the VSD to the aorta & blood from the RV flows mainly to the pulmonary artery, yielding physiology similar to Tetrology of Fallot.

In DORV with a subpulmonic VSD,(called Taussig-Bing syndrome), blood from the LV flows through the VSD to the pulmonary artery and blood from the RV flows mainly to the aorta , yielding physiology similar to Transposition of Great Arteries.

Page 5: D o r v

But if there is pulmonic stenosis in addition, physiology resembles Tetrology of Fallot

In other forms of DORV, blood from both ventricles is substantially mixed in the RV, yielding physiology that resembles a large VSD But again, if there is pulmonic stenosis, physiology resembles Tetrology of Fallot.

Page 6: D o r v

Treatment

Total corrective surgery is the definite treatment

Surgical repair includes correction of pulmonary stenosis if present & patch closure of the VSD, placed in such a way as to direct blood flow from the left ventricle to the aorta.

Palliative surgery

Page 7: D o r v

Thank You…

Deepa Merin Kuriakose

Assistant ProfessorGovt. College of

Nursing, Kottayam