86416809-Soft-Tissue-Sarcoma.ppt

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    LONGCASE SUBDIVISI BEDAH ONKOLOGI

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    Jaringan lunak jaringan selaintulang, epitel organ dala, epitel

    !ulit, siste "eatopoeti!, dan SS#Sarkoma jaringan lunak tuor

    ganas pada jaringan luna! $u!osa,sera%ut, lea!, otot polos, otot luri!,

    esotel, sino&iu, jaringanesen!i li'angial(

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    )ale * +eale ratio -,- * -,.Usia

    / 0. ta"un

    1.,2 30.45. ta"un 12,5 3

    6 5. ta"un 7-,2 3

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    No Jaringan Asal Bentuk Maligna

    1 Fibrous Fibrosarcoma

    2 Fibrohistiocytic Malignant fibrous histiocytoma

    3 Lipomatous Liposarcoma4 Smooth muscle Leiomyosarcoma

    5 Skeletal muscle Rhabdomyosarcoma

    !lood "essel #ngiosarcoma

    $ Lymph "essel Lymphangiosarcoma

    % &eri"ascular Malignant hemangio pericytoma

    ' Syno"ial Syno"ial sarcoma

    1( &araganglionic Malignant paraganglioma

    11 Mesothelial Malignant sch)annoma

    12 *+tra skeletal cartilaginous andosseous

    *+traskeletal chondrosarcoma*+traskeletal osteosarcoma

    13 &luripotential mesenchymal Malignant mesenchymoma

    14 ,eural - ,euroblastoma- *+traskeletal -s sarcoma

    15 Miscellaneous - #l"eolar soft part sarcoma- *pithelioid sarcoma- Malignant e+tra renal rhabdoid

    tumor.esmoplastic small cell tumor

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    T Primary tumor8. No e&iden9e o' priar: tuor8- 8uor /7 9 in greatest diension8-a Super;9ial tuor8-% Deep tuor

    81 8uor 67 9 in greatest diension81a Super;9ial tuor81% Deep tuor

    N Regional lymph nodesN. No regional l:p" node etastasis

    N-

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    Stage IA Lo= grade 8-a N. ).Lo= grade 8-% N. ).

    Stage IB Lo= grade 81a N. ).

    Lo= grade 81% N. ). Stage IIAHig" grade 8-a No ).

    Hig" grade 8-% N. ). Stage IIBHig" grade 81a N. ). Stage III Hig" grade 81% N. ). Stage IV An: An: 8 N- ).

    An: An:8 An: N)-

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    Kelu"an utaa tergantung predile!situor

    N:eri, %enjolan, disertai perdara"an GI,gangguan neuro&as!uler

    Seja! !apan gejala un9ulA=al un9ul, si'at pertu%u"an tuorKelu"an %er"u%ungan dengan in;ltrasi

    > pene!anan jaringan se!itarKelu"an %er"u%ungan etastasis jau"pe%esaran KGB

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    +oto polos enilai in;ltrasi tulang)

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    Lesi etastasis tunggal opera%el >rese!ta%el !eoterapi

    Dooru%i9in o%at tunggalKeoterapi !o%inasi Dooru%i9in

    I'os'aideKo%inasi lain *

    Dooru%i9in Da9ar%aine C:VADIC

    Dooru%i9in I'os'aide )esna Da9ar%aine

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    U!uran tuor 6 7 9 le%i" %uru! dan

    sering etastasis Lo!asi e!streitas prognosis le%i" %ai!

    Kedalaan le%i" super;sial prognosisle%i" %ai!

    Stadiu "istologi G- prognosis le%i" %ai!

    Lo= grade / -73 etastasisHig" grade 7.3 etastasis