THEY ARE SUGAR CONTAINING LIPIDS. THEY ARE DERIVED FROM SPHINGOLIPDS. THEY DO NOT CONTAIN...

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Transcript of THEY ARE SUGAR CONTAINING LIPIDS. THEY ARE DERIVED FROM SPHINGOLIPDS. THEY DO NOT CONTAIN...

THEY ARE SUGAR CONTAINING LIPIDS. THEY ARE DERIVED FROM SPHINGOLIPDS. THEY DO NOT CONTAIN PHOSPHATE. GLYCOLIPIDS ARE WIDELY DISTRIBUTED IN OUR BODY,PARTICULARLY IN NERVOUS TISSUE SUCH AS BRAIN CEREBROSIDES SULFATIDES GLOBOSIDES GANGLIOSIDES IT IS THE SIMPLEST GLYCOLIPID IT IS FOUND IN HIGH CONCENTRATION IN NERVE TISSUE MEMBRANE. Eg.GALACTOCEREBROSIDE THEY ARE CEREBROSIDE IN WHICH THE MONOSACCHARIDE CONTAINS A SULFATE ESTER Eg. SULFOGALACTOCERAMIDE THEY ARE IMPORTANT CONSTITUENT OF RBC MEMBRANE AND DETERMINANTS OF ABO BLOOD GROUP SYSTEM. THEY ARE INVOLVED IN CELL MEMBRANE RECEPTORS FOR CERTAIN POLYPEPTIDE HORMONES. THEY ARE IMPORTANT IN CELL ADHESION RECOGNITION. AS RECEPTORS FOR BACTERIAL TOXINS (Eg. THE TOXIN THAT COLERA). ABO BLOOD GROUP SUBSTANCES. IMPORTANT CONSTITUENTS OF THE NERVOUS TISSUE SUCH AS BRAIN. ON CELL MEMEBRANE OF RED BLOOD CELL OLIGOSACCRIDES THAT DETERMINE THE SPECIFC NATUER OF THE ABO SUBSTANCES APPEAR TOBE PRESENT IN GLYCOSPHINGOLIPIDS SPHINGOSINE CERAMIDE GLUCOCRERBROCYTE GALACTOCEREBROSIDE UDP-GLUCOSE UDP UDP-GALACTOSE UDP GANGLIOSIDE GLOBOSIDE SULFATIDES UDP-SUGARS CMP-NANA PAPS UDP-SUGARS FORMED FROM CERAMITE. THE AMINO GROUP OF SPHINGOSINE BACK BONE IS ACYLATED BY A C FATTYACID OCCUR IN MANY GLYCOSPHINGOLIPIDS,CEREBROSIDE,SULFATEIDES,GLBOSIDES,GANGLOSIDES,ARE THE DIFFERENT TYPES OF GLYCOLIPIDS. IN A CEREBROSIDE GLUCOSE OR GALACTOSE IS LINKED TO THE TERMINAL GROUP OF CERAMIDE TO FORMGLUCOCEREBROSIDE. 24 CERAMIDE REACTS WITH UDP-GLUCOSE TO FORM GLUCOCERBROSIDE. GLALCTOCEREBROSIDE REACTS WITHACTIVE SULPHATE 3- PHOSPHOADENOSINE 5-PHOSPHOSULFATE TO FORM SULFATIDES.ADDITIONAL SUGARS MAY BE ADDED TO CERAMITES TO FORM GLOBOSIDES GAUCHERS DISESSE TAY-SACHS DISEASE THEY ARE DUE TO GENETIC DEFECT IN THE PATHWAY OF GLYCOLIPID DEGRADATION IN THE LYSOSOMES